Spinal Dysraphism: Trends in Northern India

Kumar, Raj; Singh, Sanjay

doi:10.1159/000068819

Cited by 70 publications

(67 citation statements)

References 18 publications

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“…Thus, localized hypertrichosis may be a clue for an underlying defect, some of which are surgically correctable at an early age. Sacral hypertrichosis is also known as faun tail naevus, and this is the most common skin lesion that is evident at birth 11 , as was seen in our patient. Hairy patches are most frequently associated with tethered cord and diastematomyelia 12 .…”

Section: Discussionsupporting

confidence: 71%

A Case of Faun Tail Naevus Treated by Intense Pulsed Light

et al. 2009

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Section: Discussionsupporting

confidence: 71%

A Case of Faun Tail Naevus Treated by Intense Pulsed Light

et al. 2009

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“…6 In a study conducted in Lucknow, India, meningomyeloceles accounted for 72% of the cases, meningocele in 2%, myelocystocele in 2% and 23% had occult spina bifida (split cord malformation without overt MMC sac 19% and midline dermal sinus in 4.5%). 7 A lower incidence of split cord malformation ( 7% of the cases) and dermal sinus (1% of the cases) of was recorded by us. Meningomyelocoeles accounted for majority of the cases and accounted for 72% of the cases which is similar to literature gathered.…”

Section: Discussionmentioning

confidence: 66%

Study of clinical profile and associated anamalies and surgical outcome of spina bifida

2017

Int Surg J

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Background: Neural tube defects (NTDs) are a group of congenital anomalies characterized by defects in dorsal midline structures, including neural tissue, dura, muscle, bone and/or skin. The clinical presentations and the followup of these patients require attention to various end organs besides the nervous system. The aim was to evaluate the clinical profile and surgical outcome of children with spina bifida. Methods: Out of a total of 74 patients treated at our institute for spina bifida between June 2013 to August 2015, 74 cases of spina bifida were analyzed retrospectively and prospectively. The clinical profile, radiological findings and urodynamic studies were recorded. Craniospinal MRI was done in patients to screen for Arnold Chiari malformations and monitoring of hydrocephalus was done as a management protocol at our institute for these children. All these patients except two underwent surgery for correction and closure of the spinal defect. Associated anomalies were treated accordingly. They were clinically assessed over a mean follow up period of 11months ranging from 2months to 2 ½ years. Results: 73% of the patients presented in the neonatal age group. Of which, 72% presented with a visible sac over the back.72% of the cases were myelomeningocoeles. 79% of the defects were in the lumbosacral region. 30% presented with sensorimotor loss or bladder bowel incontinence. Sensorimotor improvement was seen in 12.5% after repairing the defect with the help of physiotherapy and braces. 30% of the patients were diagnosed to have hydrocephalus, of which 33% required a CSF diversion procedure. The postoperative course of spina bifida repair was found to be uneventful in 90% of the patients. Conclusions: A multidisciplinary approach is required to address this disease. Early diagnosis, surgical management and rehabilitation can prevent further neurological damage and can improve quality of life in patients with spina bifida.

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“…14 Peak occurrence of diastemetomyelia was in 0-10 yr age group and common in female. Study by previous researchers 10,11 state that spit cord malformations common in females. One researcher stated that, dermal sinus is epithelium lined fistula that extends inward from skin surface and can connect with central nervous system ant the meningeal coating and is shown in Figure 3.…”

Section: Occult Spinal Dysraphismmentioning

confidence: 92%

Spinal dysraphism: MRI evaluation

Ramacharya

Desai²

2015

Int J Res Med Sci

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INTRODUCTIONSpinal cord development occurs through three consecutive stages, gastrulation (gestational weeks 2-3) with formation of notochord, primary neurulation (weeks 3-4) produces the upper most nine tenths of the spinal cord and secondary neurulation and retrogressive differentiation (weeks 5-6) result in formation of the conus tip and filum terminale. Defects in these early embryonic stages produce spinal dysraphism. Spinal dysraphism refers to the entire range of spinal column and neuraxis anomalies. 1 Open spina bifida /aperta includes myelocele, myelomeningocele ( Figure 1) and hemimyelomeningocele and hemimyelocele.Occult spinal dysraphism includes skin-covered masses suchas lipomyelomeningocele (Figure 2), skin-covered meningoceles or myelocystoceles and the group of spinal dysraphism without an associated mass. This group encompasses dorsal dermal sinus (Figure 3), spinal lipoma, tethered cord (tight filum terminale syndrome), and fibrolipoma of the filum terminale, diastematomyelia and anterior-sacral-meningocele.Prevalence: The estimated incidence of spinal dysraphism is about 1-3/1000 live births. 3 The prevalence of spinal dysraphism has been in decline the world over in the last ABSTRACT Background: Spinal dysraphism refers to the entire range of spinal column and neuraxis anomalies. The objective was to evaluate the role of magnetic resonance imaging (MRI) in characterizing the congenital and developmental disorders of spine. Methods: Fifty (50) patients with clinically suspected spinal dysraphism were included in the study. All the patients were made to undergo MRI spine using 1.5 Tesla MRI, manufactured by GE, SIGNA HDX MACHINE. The findings of MRI spine were assessed and analyzed. Results: Out of 50 patients included in the study; 24 were male (48%) and remaining 26 were female (52%). Congenital spinal lesions were more prevalent in the age group 0-20 years (70%). Lesions without subcutaneous masses (62%) were more common than the lesions with subcutaneous masses (38%). The commonest location for the congenital spinal lesions was lumbar region (54%). Congenital spinal lesions without spinal curvature abnormalities (58%) were more common than the lesions with spinal curvature abnormalities (42%). Vertebral anomalies (78%) were the commonest spinal anomalies in patients with congenital spinal lesions; spina bifida was the commonest (46%). Diastematomyelia was more prevalent in the age group 0-10 years (41.66%) and in female population (58.33%). Conclusion: Thus we conclude that Spinal dysraphism were common in young females, with commonest anomaly being vertebral anomaly (Spina bifida), commonest location is lumbar region, Diastematomyelia common in young aged female. Magnetic resonance imaging is an accurate, noninvasive, safe and advanced modality for evaluation of the congenital spinal disorders and help in better management of these patients with prompt and accurate diagnosis.

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Spinal Dysraphism: Trends in Northern India

Cited by 70 publications

References 18 publications

A Case of Faun Tail Naevus Treated by Intense Pulsed Light

A Case of Faun Tail Naevus Treated by Intense Pulsed Light

Study of clinical profile and associated anamalies and surgical outcome of spina bifida

Spinal dysraphism: MRI evaluation

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