“…The asplenia anomaly is significantly more common in males than females [Van Mierop et al, 1972;Rose et al, 19751. In addition to the cardiovascular anomalies, which usually suggest the prognosis, there are frequently related extracardiac malformations such as bronchopulmonary, gastrointestinal, genitourinary, central nervous system, skeletal, and endocrine anomalies [Freedom, 1972;Van Mierop et al, 1972;Rose et al, 1975;Van Went et al, 1977;Mishalany et al, 19821.…”