Sphenoid dysplasia in neurofibromatosis type 1: a new technique for repair

Abstract

Sphenoid bone dysplasia in NF1, resulting in proptosis and exophthalmos, is usually progressive. It can be surgically repaired using a curved titanium mesh with the convexity faced to the temporal pole that is in the opposite fashion from all the techniques previously introduced. When utilized early in life, the technique can prevent the occurrence of the orbital and facial disfiguration.

Reconstruction of Sphenoid Wing Dysplasia in Neurofibromatosis Type-1 Patients: An Evolving Technique

“… 4 Therefore, new techniques have been developed including the use of titanium mesh covered by lyophilised dura, which is reported to prevent the adherence of the mesh and the passage of meningoencephalocele through its permeations. 5 In our series, we have not had any implant-related infections, and we believe that in the presence of healthy vascularised soft tissue cover, the risk is small.…”

Neuroimaging findings of extensive sphenoethmoidal dysplasia in NF1

“…The use of traditional split bone grafts in repair of SWD in NF1 have been associated with bone resorption and recurrence of symptoms [24,25]. Titanium mesh repair solves the problem of bone resorption but can be associated with graft infection, development of adhesions, and recurrence of dural herniation through the mesh [23,26,27]. Newer techniques include reconstruction with the use of high density porous polyethylene (HDPP) implants, which have produced stable results with no displacement or resorption [26].…”

Reconstruction of the Sphenoid Wing in A Patient with Sphenoid Wing Dysplasia in NF1 – A Case Report

“…The reconstruction can be done from the cranial side 3 , or from the orbital side with radial titanium mesh 2 . Another process is to use a reverse curved titanium mesh 11 . We have used the transcranial route as it was more convenient for us and placed an extradural titanium mesh.…”