Spheno-orbital encephalocele

Intraorbital Encephalocele Presenting with Exophthalmos and Orbital Dystopia : CT and MRI Findings

“…Encephaloceles are classified according to their intracranial localizations and basal encephaloceles are classified under 5 main headings according to their localizations including spheno-ethmoidal, trans-sphenoidal, spheno-orbital, transethmoidal and spheno-maxillary 6 , 7) . Absence of the sphenoidal wings leads to spheno-orbital encephaloceles and brain tissue and menings protrude to orbital cavity through superior orbital fissure 2 , 6) . Increased herniation due to the dural defects and the absence of the limited effect of the bone during physiologic growing of the brain and the cranium, continuous pulsation of the brain are the accepted mechanisms of the enlargement of the bone defect 7) .…”

“…Encephaloceles are classified according to 5 anatomic sites, namely the spheno-ethmoidal, transsphenoidal, spheno-orbital, transethmoidal and sphenomaxillary 6) . Congenital absence of portions of the wings of the sphenoid leads to spheno-orbital encephalocele, a rare entity in the literature 2) . We wanted to share this case who had not seen any treatment until puberty and being purely congenital as being not related to trauma or neurocutaneous syndrome and also in the literature review there isn't any case like our case.…”