Spectrum of clinical presentations of vein of Galen aneurysm

Sasidharan, C. K.; Anoop, Parameswaran; Vijayakumar, M.; Jayakrishnan, M. P.; Reetha, G.; Sindhu, Thekkile Gangadharan

doi:10.1007/bf02725643

Cited by 19 publications

(22 citation statements)

References 18 publications

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“…Au niveau cardiaque, le shunt vasculaire à débit élevé est responsable d'une défaillance cardiaque dont la gravité est corrélée à l'importance du shunt [2,8,12]. Quelques malformations cardiaques peuvent s'associer à l'AVG à savoir la coarctation aortique, le sinus venosus et la communication interauriculaire [5]. In utero, les conséquences de ce shunt sont plus atténuées du fait que les résistances placentaires basses protègent le foetus par un phénomène de compétition avec les résistances basses de la fistule [9,10].…”

Section: Discussionunclassified

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Forme sévère d’un anévrisme de la veine de Galien compliquée d’encéphalomalacie de révélation anténatale

et al. 2011

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Section: Discussionunclassified

“…Elle représente moins de 1 % des malformations artérioveineuses cérébrales congénitales [1][2][3][4]. Elle se révèle à l'âge néonatal dans 40 à 50 % des cas [2,5], le plus souvent par un tableau d'insuffisance cardiaque. La malformation est rarement découverte in utero.…”

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Forme sévère d’un anévrisme de la veine de Galien compliquée d’encéphalomalacie de révélation anténatale

et al. 2011

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“…In adults, this pathology has been described by some authors 3,6,7,[14][15][16][17][18][19][20] . Because of its rarity in adults, and despite what is known from these studies, there is still insufficient information about this disease during adult age 13 .…”

Section: Discussionmentioning

confidence: 99%

“…The indications of these treatments are based on case-specific clinical manifestations 9 . Sasidharan et al 20 , suggested conservative conduct and patient monitoring for those with severe heart failure. The absence of blood flow at the deep cerebral venous system due to malformation thrombosis, absence of signs or symptoms of intracranial hypertension, and pharmacological control of seizures led us to conservative treatment of the patient presented here.…”

Section: Discussionmentioning

confidence: 99%

Vein of Galen aneurysm in an adult: case report

Lobão

Sassaki

et al. 2006

Arq. Neuro-Psiquiatr.

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-Vein of Galen aneurysm is a rare pathology, representing less than 1% of intracranial vascular malformations. We report on a 65 years-old man who experienced a generalized tonic-clonic seizure. Brain imaging showed a large calcified expanding mass in the pineal region, confirming the diagnosis of a vein of Galen aneurysm. Because of the spontaneous thrombosis of the malformation, there was no need for microsurgical or endovascular treatment and he is been regularly followed since that.KEY WORDS: vein of Galen aneurysm, vein of Galen malformation, cerebral vein, congenital vascular malformation. Aneurisma da veia de Galeno em adulto: relato de casoRESUMO -Aneurisma da veia de Galeno é patologia rara, representando menos de 1% das malformações vasculares intracranianas. Apresentamos o caso de um homem de 65 anos que teve episódio de crise convulsiva tônico-clônica generalizada. Exames de imagem evidenciaram grande processo expansivo calcificado na região pineal, confirmando o diagnóstico de aneurisma trombosado de veia de Galeno. Devido à trombose espontânea da malformação, foi excluída a possibilidade de tratamento endovascular bem como microcirúrgico, mantendo-se o acompanhamento clínico. PALAVRAS-CHAVE: aneurisma da veia de Galeno, mal-formação da veia de Galeno, veias cerebrais, malformação vascular congênita.Vein of Galen aneurysm (VGA) is a rare vascular malformation representing less than 1% of vascular intracranial abnormalities. It is a congenital process frequently detected between the 6 th and 11 th months of gestational age 1 , during early childhood or neonatal period 2 . This finding in adult age is very rare, presenting or not symptoms throughout childhood 3 . Clinical manifestations can present at any age in the form of heart failure, delayed neuropsychomotor development, hydrocephalus and seizures 4 .We describe a case of VGA reporting clinical symptoms, radiological findings and management relating to current published literature. CASEA 65 year-old man was brought to the emergency room at the University Hospital of the Pontifical Catholic University of Paraná, Brazil because of generalized tonic-clonic seizures. On admission, he was treated with anticonvulsant therapy for status epilepticus. Past medical history was significant for treated high blood pressure and heart failure diagnosed late in life. Also significant for an episode of ischemic cerebrovascular disease two years before, resulting in left hemiparesis. During childhood and adult life there was no neuropsycomotor development delay, no signs of cardiopathy, no neurological signs or symptoms as well as no history of epilepsy.CT scan showed a calcified expanding process in the pineal region (Fig 1). MRI showed a heterogenic roundshaped mass localized in the supra-vermian cistern with dimensions of 35x32x30 mm showing high signal in T2-weight imaging (Fig 2). The MRI images were suggestive of a thrombosed VGA. Cerebral angiography showed a thrombosed VGA also (Fig 3).Considering the fact that the aneurysm was already thrombosed ...

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“…3,5 Mortality rates are reported between 50% and 100% for neonates. 4 Survivors often have severe mental and neurologic limitations.…”

Section: Answer To Diagnostic Challenge (From Page 43) a Hole In The mentioning

confidence: 99%

Diagnostic Challenge

Moore

Gonzales²,

Brogdon³

2008

Journal of Diagnostic Medical Sonography

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A 17-year-old, gravida 1, para 0, with an uncomplicated pregnancy and an unsure last menstrual period presented for a routine level II scan to establish dates and to rule out anomalies. Biometry was consistent with a 28-week gestation. On that initial scan, Figures 1 and 2 were obtained.Color Doppler interrogation demonstrated no vascularity. There were no other anomalies. The patient was asked to return in four weeks for growth and to reevaluate the fetal brain.

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Spectrum of clinical presentations of vein of Galen aneurysm

Cited by 19 publications

References 18 publications

Forme sévère d’un anévrisme de la veine de Galien compliquée d’encéphalomalacie de révélation anténatale

Forme sévère d’un anévrisme de la veine de Galien compliquée d’encéphalomalacie de révélation anténatale

Vein of Galen aneurysm in an adult: case report

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