Solitary neurofibroma of the trachea

Abstract

The patient was a 60-year-old white male who, for 18 months, had complained of a substernal wheeze on exertion, exertional dyspnoea and cough, and attacks of acute respiratory distress. There was no haemoptysis or dyshpagia and he was treated for bronchial asthma until bronchoscopy revealed the tumour which had not been recognized in plain chest films. He showed no evidence of a neurofibromatosis and apart from reduction in pulmonary function tests on a PO2 of 74, his laboratory tests were negative. There was no family history of neurofibromatosis. He underwent thoracotomy and a smooth rounded pedunculated tumour, 2.5 cm in diameter, arising from the posterior wall of the trachea, 3 cm above the carina was excised. He has had no tumour recurrence.

Endotracheal neurofibroma in a patient with von Recklinghausen's disease

“…In two cases, the classic cutaneous von Recklinghausen's disease was present. The clinical presentation of these patients is similar to that caused by other tracheal tumours [3,[5][6][7]. In only two cases were endotracheal neurofibromas identified on chest roentgenograms.…”

Late Presentation of Giant Intrathoracic Neurofibroma with Significant Mediastinal Shift: A Case Report and Review of the Literature

“…However, there are also reports in the literature of neurofibromas arising from trachea and oesophagus [12, 13]. …”

Anesthetic management of a patient with tracheal neurofibroma

“…Computerized axial tomographic scan showed a 4-cm smooth tumor arising mainly from the right lateral wall of the trachea and extending into the lumen, narrowing the tracheal lumen. Neurofibromas of the trachea can be associated with NF-1 or independently [3][4][5]. Neurofibromatosis can involve the bronchi and lungs.…”