Small Intestinal Scleroderma With Malabsorption and Pneumatosis Cystoides Intestinalis

Meihoff, Walter E.; Hirschfield, Jan S.; Kern, Fred

doi:10.1001/jama.1968.03140230012003

Cited by 40 publications

(4 citation statements)

References 9 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…In many circumstances, pneumatosis cystoides intestinalis is a benign condition, but in SSc, it may be associated with rapidly progressive SSc and death (77). It is important to distinguish benign intraperitoneal gas associated with pneumatosis from that associated with an intraabdominal catastrophe for which emergent surgery is indicated (78).…”

Section: The Stomach and Small Intestinementioning

confidence: 99%

“…In addition to gastroparesis, pseudoobstruction, and malabsorption, the following other intestinal presentations of SSc have been reported: pneumatosis cystoides intestinalis, small intestine telangiectasia, and small bowel diverticula. In many circumstances, pneumatosis cystoides intestinalis is a benign condition, but in SSc, it may be associated with rapidly progressive SSc and death (77). It is important to distinguish benign intraperitoneal gas associated with pneumatosis from that associated with an intraabdominal catastrophe for which emergent surgery is indicated (78).…”

Section: Chronic Intestinal Pseudoobstructionmentioning

confidence: 99%

See 1 more Smart Citation

Gastrointestinal motility disorders in scleroderma

Sjogren

1994

Arthritis & Rheumatism

335

228

View full text Add to dashboard Cite

Section: The Stomach and Small Intestinementioning

confidence: 99%

Section: Chronic Intestinal Pseudoobstructionmentioning

confidence: 99%

Gastrointestinal motility disorders in scleroderma

Sjogren

1994

Arthritis & Rheumatism

335

228

View full text Add to dashboard Cite

“…Our patient presented a considerable management problem. There are few treatments available for intestinal hypomotility or pneumatosis other than conservative approaches such as permanent parenteral nutrition (9), dietary therapy (9-1 1), antibiotics to reduce bacterial overgrowth (9,10,12), Dpenicillamine (13), and oxygen (6). A successful outcome is rare in such patients.…”

Section: Discussionmentioning

confidence: 99%

Response to Octreotide of Intestinal Pseudoobstruction and Pneumatosis Cystoides Intestinalis Associated with Progressive Systemic Sclerosis.

Kobayashi

Naka

et al. 1993

Intern. Med.

View full text Add to dashboard Cite

Intestinal pseudoobstruction and pneumatosis cystoides intestinalis are uncommon complications of progressive systemic sclerosis. Wereport a 26-year-old womanwith this disorder who responded poorly to conventional treatment. Subcutaneous administration of octreotide, a longacting somatostatin analogue, at a dose of50 J^g/day for 3 weeks, relieved symptoms such as nausea and bloating. There was also a markeddecrease of intestinal gas accumulation, as documentedon X-ray films. (Internal Medicine 32: 607-609, 1993)

show abstract

“…The condition is known as pneumatosis cystoides intestinalis or coli depending on the extent of disease process. It may be idiopathic (Koss, 1952) or associated with other diseases including pulmonary disease (Botsford and Krakower, 1938;Doub and Shea, 1960), pyloric stenosis (Dhall et al, 1968), malignant conditions (Finney, 1908;Dale and Pearse, 1950;Williams et al, 1963;Thorpe, 1965), collagen diseases (Meihoff et al, 1968, White et al, 1970Mueller et al, 1972), adhesions from previous surgery (Koss, 1952), and occurs after long-term administration of practolol (Thein and Asquith, 1977).…”

mentioning

confidence: 99%