Siringomielia no secundaria a Chiari. Actualización en fisiopatología y manejo

Giner, Javier Micó; López, Carlos Pérez; Hernández, B.; Riva, Á. Gómez de la; Isla, Alberto; Roda, J.M.

doi:10.1016/j.nrl.2016.09.010

Cited by 16 publications

(4 citation statements)

References 31 publications

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“…The pathophysiology of syringomyelia is uncertain. However, several hypothetical theories have been postulated to explain the development of syringomyelia [3,11]. Syringomyelia has been associated with noninfectious inflammatory lesions [12].…”

Section: Discussionmentioning

confidence: 99%

“…The clinical course progresses over months to years with an early rapid deterioration that wanes over time [13]. Although there are no specific symptoms associated with syringomyelia, sensory abnormalities, motor weakness, and pain are the most common manifestations [3].…”

Section: Discussionmentioning

confidence: 99%

“…It is most frequently associated with Chiari 1 malformation, which accounts for half of the cases. Other causes include trauma, spinal cord tumors, post-inflammatory cord lesions, and secondary myelomalacia [3].…”

Section: Introductionmentioning

confidence: 99%

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Coexistence of Systemic Lupus Erythematosus and Syringomyelia: A Case From a Rural Center in Nigeria

Emorinken¹,

Erameh²,

Eluehike³

et al. 2021

Cureus

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Systemic lupus erythematosus and syringomyelia are two distinct conditions with different pathogenetic pathways as well as diverse genetic and clinical characteristics. The coexistence of these two conditions has not been previously documented in the literature. We describe a 38-year-old male who presented with progressive bilateral weakness and pain in the lower limbs and loss of sphincteric functions three years following a diagnosis of lupus nephritis. Relevant autoantibody testing, hypocomplementemia, and biopsyproven membranous lupus nephritis confirmed the diagnosis of systemic lupus erythematosus and magnetic resonance imaging of the spine confirmed the presence of syringomyelia. Therapy for lupus nephritis was instituted accordingly, while the patient was referred for neurosurgical intervention. The mechanism underlying syrinx formation in this patient is uncertain and, thus, further research is critical in this area.

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Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

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Coexistence of Systemic Lupus Erythematosus and Syringomyelia: A Case From a Rural Center in Nigeria

Emorinken¹,

Erameh²,

Eluehike³

et al. 2021

Cureus

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“…Enlargement of the fluid-filled cavity within the spinal cord often results in the clinical course of progressive neurologic deficit, such as sensory loss, pain, motor weakness, and autonomic dysfunction 2 . Many papers have been published on syringomyelia related to Chiari malformation, but little is known about idiopathic syringomyelia, which requires specific management 3 . Over years, numerous theories have attempted to explain the pathogenesis of syringomyelia.…”

Section: Introductionmentioning

confidence: 99%

Minimally Invasive Treatment of Idiopathic Syringomyelia Using Myringotomy T-Tubes: a Case Report and Technical Note

Jugović

Bošnjak

Rotim

et al. 2020

ACC

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-Syringomyelia is characterized by a fluid-filled cavity within the spinal cord. Expansion of the syrinx often results in the clinical course of progressive neurologic deficit. Surgery for syringomyelia generally aims to treat the underlying cause, if it is known. However, little is known about idiopathic syringomyelia, which requires specific management. In our paper, an alternative, minimally invasive treatment option for large symptomatic idiopathic cervicothoracic syrinx is described and discussed. We present a case of a 44-year-old male without a history of spinal cord trauma, infection, or other pathologic processes, who presented for thoracic pain. Due to progressive pain and left leg paresis, magnetic resonance imaging (MRI) was performed and revealed extensive septated syringomyelia from T5 to T7 and hydromyelia cranially. We applied minimally invasive technique for shunting the idiopathic syrinx into the subarachnoid space using two Richards modified myringotomy T-tubes. Postoperative MRI revealed significant decrease in the syrinx size and clinical six-month follow-up showed improvement of clinical symptoms. This minimally invasive treatment of syringomyelia was found to be an effective method for idiopathic septated syrinx, without evident underlying cause. However, long-term follow-up and more patients are necessary for definitive evaluation of this technique.

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