Congenital inguinal hernia is a very important subject for both general and pediatric surgeons, and many issues related to the inguinal hernia in infants and children are still confusing. Herein, the subject of congenital inguinal hernia, including the relevant embryology, related anatomy, the symptoms and signs essential for diagnosis, and the needed examination tests and investigations, is presented in a systematic manner. Also, the updated treatment options were discussed including both open and laparoscopic approaches with spotlight on the very recent single incision laparoscopic inguinal hernia repair in children. Finally, at the end of the chapter, there are many valuable references for more details.