Síndrome de vasoconstricción cerebral reversible secundario a un paraganglioma yugular secretor de metanefrinas

Reversible Cerebral Vasoconstriction Syndrome Associated with a Suprarenal Mass

“…This case illustrates the classic clinical presentation of RCVS. Thunderclap headache is usually the typical symptom with or without neurological focalization and the diagnostic criteria suggested by Calabrese et al (2007) propose that headache should be associated with diffuse changes in the tone of the cerebral vasculature documented by angiography (De Angelis et al, 2018;Arenas-Beltrán et al, 2019). Because it is usually associated with medical conditions, a classification dividing the aetiology of the syndrome between idiopathic and symptomatic has been purposed (Coral and Roa, 2009).…”

“…There are some cases describing the association between the appearance of tumours and RCVS (Mathis et al, 2017;Arenas-Beltrán et al, 2019). Paragangliomas are the most frequent association that has been reported (Arenas-Beltrán et al, 2019).…”

“…There are some cases describing the association between the appearance of tumours and RCVS (Mathis et al, 2017;Arenas-Beltrán et al, 2019). Paragangliomas are the most frequent association that has been reported (Arenas-Beltrán et al, 2019). Although there is a clear physiopathological association between tumours producing vasoactive agents, the most frequently reported cases are of nonsecretory tumours ass less than 5% of the paragangliomas secrete catecholamines (Mathis et al, 2017) paraganglioma may affect the carotid body (carotid body tumour.…”

“…Although there is a clear physiopathological association between tumours producing vasoactive agents, the most frequently reported cases are of nonsecretory tumours ass less than 5% of the paragangliomas secrete catecholamines (Mathis et al, 2017) paraganglioma may affect the carotid body (carotid body tumour. As sixty percent of head and neck parangangliomas are carotid body tumours, situated at the bifurcation of the common carotid artery, it is accepted that they can compromise the baroreceptor reflex triggering trigger hypertension, headache and tachycardia (Mathis et al, 2017;Arenas-Beltrán et al, 2019).…”

“…Cases have been described in the literature with producing and non-producing masses of metanephrines (Mori et al, 2012;Duke and Ullrich, 2018;Katada et al, 2018;Arenas-Beltrán et al, 2019). Within these reports, associations with cavernous haemangioma, medulloblastoma, colon cancer, paraganglioma, pheochromocytoma, uterine fibroids, among others were found (Mori et al, 2012;Duke et al, 2018;Katada et al, 2018;Arenas-Beltrán et al, 2019). However, no association with adrenal masses which do not produce metanephrines was found.…”