Síndrome de Prune Belly

Abstract

Prune Belly Syndrome is a fetal uropathy of unknown etiology with incidence of 1/35000 to 1/50000 alive been born, characterized by a classical triad: abdominal musculature congenital deficiency, bilateral criptorquidia and urinary tract malformations. The authors present a case of this rare pathology associated with a patent urachus. After complementary exams confirmed urinary tract alterations (bilateral ureterohidronefrosis and vesicoureteral reflux degree 5, besides urinary infection), the surgical approach was vesicostomy to decrease urinary infections and sepsis. Definitve surgery should be accomplished around the 12 th month of life. Nowadays, the child is asymptomatic , with follow-up every two months, with return consultation bimonthly (Rev. Col. Bras. Cir. 2004; 31(6): 400-401).

Pregnant patient with prune belly syndrome: case report

“…The absence of fetal abdominal musculature caused spinal instability and chest deformity in the patient of this case, compromising lung development. (1,3) Also, a maternal pelvic rotation did not allow for vaginal insinuation or descent of the fetus, which, together with the transverse presentation, was responsible for the indication of a cesarean section. Elective preterm delivery occurred due to the maternal risks of uterine rupture and the risks of fetal distress due to fetal weight near the 3 rd percentile.…”