Simultaneous juvenile polyposis syndrome and neurofibromatosis type 1 – Response to Letter to the Editor

Agaimy, Abbas

doi:10.1111/his.12749

Cited by 1 publication

(2 citation statements)

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“…In cases where multiple true juvenile polyps in an NF1 patient are suggested with limited clinical information and biopsy specimens, the coexistence of NF1 and juvenile polyposis should be considered 3 even though this situation is extremely rare. 2 In conclusion, we presented a case of surgical resection for a polyp that may be the same as those reported by Agaimy et al 1 in the present report. The lesion was both a mucosal and submucosal inflammatory polyp composed of stromal proliferation, which was overall similar to IFPs rather than to juvenile polyps or hyperplastic polyps.…”

Section: Discussionsupporting

confidence: 88%

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Neurofibromatosis Type 1–Associated Inflammatory Polyp of the Gastrointestinal Tract

2016

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The entity known as "juvenile-like (inflammatory/hyperplastic) mucosal polyps of the gastrointestinal tract in neurofibromatosis type 1 (NF1)" was recently proposed, but is not well known. Here, we describe the characteristics of this entity in a surgically resected case. The hemorrhagic 2 × 1 cm-sized polyp was resected from the ascending colon of a 55-year-old male NF1 patient. The polyp was composed of characteristic multiple mucosal protrusions and submucosal elements that included vasculopathic changes. Histologically, this lesion was similar to an inflammatory fibroid polyp rather than juvenile or hyperplastic polyps. This disease could be a distinct entity, and "inflammatory vasculopathic polyp" would be a suitable name.

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Section: Discussionsupporting

confidence: 88%

“…Agaimy et al 1,2 and Brosens et al 3 reported inflammatory polyps of the gastrointestinal (GI) tract in patients with neurofibromatosis type 1 (NF1). Agaimy et al 1 reported 4 cases of lesions specific to NF1, while Brosens et al 3 considered the possibility of incidentally coexisting true juvenile polyps in NF1 patients.…”

Section: Introductionmentioning

confidence: 99%