Simultaneous arterial switch and totally anomalous pulmonary venous connection repair in a 5-hour-old child, complicated by pulmonary venous stenosis

Abstract

A 5-hour-old boy underwent arterial switch operation and totally anomalous pulmonary venous connection repair. Subsequently developed severe pulmonary venous stenosis was successfully treated with hybrid balloon angioplasty.

A situs solitus transposition of great arteries with obstructed sub-diaphragmatic totally anomalous pulmonary venous connection: a rare case treated with anatomical repair

“…Among post-mortem 12 and in vivo reports, sub-diaphragmatic drainage was the rarest form of totally anomalous pulmonary venous connection, with only three cases before ours. 5,8,11 Mykychak described the only case with the same anatomy as our report (intact ventricular septum and no other associated CHDs). 11 As in Lopes et al, 8 our first echocardiogram did not detect the totally anomalous pulmonary venous connection.…”

“…5,8,11 Mykychak described the only case with the same anatomy as our report (intact ventricular septum and no other associated CHDs). 11 As in Lopes et al, 8 our first echocardiogram did not detect the totally anomalous pulmonary venous connection. While in that report totally anomalous pulmonary venous connection was diagnosed during cardiac catheterisation, in our case a repeat echocardiogram revealed the totally anomalous pulmonary venous connection before catheterisation.…”

“…Transposition of the great arteries combined with totally anomalous pulmonary venous connection is extremely rare outside of heterotaxy syndrome. Since the first description in 1964, 1 few cases have been reported, [2][3][4][5][6][7][8][9][10][11] most have been treated by an atrial switch operation. We report the successful treatment of a neonate with transposition of the great arteries, intact ventricular septum and obstructed sub-diaphragmatic totally anomalous pulmonary venous connection, repaired by arterial switch operation and connection of the pulmonary venous return to the left atrium.…”

Complete transposition of great arteries associated with total anomalous pulmonary venous connection: An unusual cause for early left ventricular myocardial mass regression

“…[5] Recently, 2 more case reports of successful anatomic repair were reported in neonates. [67] In our case, we preferred to do atrial switch due to significantly small mitral valve annulus though some centers may still do ASO with extracorporeal membrane oxygenation support. In conclusion, complete TGA and TAPVC is a rare combination and should be suspected in cases with early LV regression along with dilated RA and RV and also in neonates presenting with high saturations with small inadequate mixing communications.…”

Comparison of Echocardiography and Computed Tomography/Magnetic Resonance Imaging for Assessing of Pulmonary Vein Stenosis in Children

“…According to our previous approach, CT/MRI imaging was performed only in complex cases [13] mostly to clarify the anatomy. Since April 2018 all patients in our institution with PVS undergo cross-sectional imaging for the veri fication of diagnosis and surveillance after repair.…”