Severe Hip Dysplasia in Wiedemann-Steiner Syndrome Treated with Bilateral Bernese Periacetabular Osteotomy

Evans, David C; Novais, Eduardo N.

doi:10.2106/jbjs.cc.21.00623

Cited by 2 publications

(3 citation statements)

References 11 publications

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Section: Discussionmentioning

confidence: 99%

“…Another study shows that some women need to use relaxin to relax the pelvic ligaments during childbirth, but relaxin can enter the fetus through the placental barrier, which may lead to relaxation of the ligaments around the acetabulum and become a potential risk of DDH in infants and young children. Adductor tension contracture is an important pathological change in children with DDH aged 0-6 months, and most Evidence-Based Complementary and Alternative Medicine hips can be reduced after release of the adductor muscle [14,15]. e prevalence of developmental dysplasia of the hip varies between different geographic regions and races, and the prevalence in China is about 1-3 per 1,000, with the incidence in girls being about 3-6 times higher than that in boys [16].…”

Section: Discussionmentioning

confidence: 99%

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Clinical Efficacy and Safety of Ibuprofen plus Traction, Reposition, and Hip Spica Cast in the Treatment of Developmental Dysplasia of the Hip

Feng

Liu

Chen

et al. 2022

Evidence-Based Complementary and Alternative Medicine

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Objective. To assess the clinical efficacy and safety of ibuprofen plus traction, reposition, and hip spica cast in the treatment of developmental dysplasia of the hip (DDH). Methods. Between January 2019 and July 2020, 60 children with DDH treaded in department of orthopedics of our institution were assessed for eligibility and recruited. They were assigned at a ratio of 1 : 1 to receive either traction + reposition + hip spica cast plus analgesia pump (observation group) or traction + reposition + hip spica cast plus analgesia pump and oral ibuprofen (control group). The outcome measures included clinical efficacy, pain scores, unexpected pain calls, the dosage of analgesia pump, and adverse events. Results. The two groups had similar clinical efficacy ( P > 0.05 ). The patients given oral ibuprofen were associated with significantly lower pain scores at 24 h and 72 h postoperatively versus those without oral ibuprofen ( P < 0.05 ). Analgesics with oral ibuprofen resulted in fewer unexpected pain calls versus analgesics without oral ibuprofen within 72 h postoperatively ( P < 0.05 ). The application of oral ibuprofen in the analgesia pump showed great improvement in lowering the dosage of analgesia pump versus the absence of ibuprofen ( P < 0.05 ). The incidence of adverse events was similar between the two groups of patients ( P > 0.05 ). Conclusion. Traction + reposition + hip spica cast plus analgesia pump and oral ibuprofen effectively mitigated postoperative pain in children with DDH and reduces analgesic drug dosage with a high safety profile.

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Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

Clinical Efficacy and Safety of Ibuprofen plus Traction, Reposition, and Hip Spica Cast in the Treatment of Developmental Dysplasia of the Hip

Feng

Liu

Chen

et al. 2022

Evidence-Based Complementary and Alternative Medicine

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“…Musculoskeletal problems are common, and these include scoliosis, craniovertebral junction anomalies, small and puffy hands and feet, brachydactyly, clinodactyly, tapering fingers with fetal finger pads, broad and short toes, rib anomalies, sacral dimples, and laxity of the distal joints. Some patients with severe scoliosis or hip dysplasia required surgery [ 18 , 19 ].…”

Section: Review Of the Literaturementioning

confidence: 99%

Wiedemann–Steiner Syndrome: Case Report and Review of Literature

Zhang

et al. 2022

Children

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Wiedemann–Steiner syndrome (WDSTS) is an autosomal dominant disorder with a broad and variable phenotypic spectrum characterized by intellectual disability, prenatal and postnatal growth retardation, hypertrichosis, characteristic facial features, behavioral problems, and congenital anomalies involving different systems. Here, we report a five-year-old boy who was diagnosed with WDSTS based on the results of Trio-based whole-exome sequencing and an assessment of his clinical features. He had intellectual disability, short stature, hirsutism, and atypical facial features, including a low hairline, down-slanting palpebral fissures, hypertelorism, long eyelashes, broad and arching eyebrows, synophrys, a bulbous nose, a broad nasal tip, and dental/oral anomalies. However, not all individuals with WDSTS exhibit the classic phenotype, so the spectrum of the disorder can vary widely from relatively atypical facial features to multiple systemic symptoms. Here, we summarize the clinical and molecular spectrum, diagnosis and differential diagnosis, long-term management, and care planning of WDSTS to improve the awareness of both pediatricians and clinical geneticists and to promote the diagnosis and treatment of the disease.

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Severe Hip Dysplasia in Wiedemann-Steiner Syndrome Treated with Bilateral Bernese Periacetabular Osteotomy

Cited by 2 publications

References 11 publications

Clinical Efficacy and Safety of Ibuprofen plus Traction, Reposition, and Hip Spica Cast in the Treatment of Developmental Dysplasia of the Hip

Clinical Efficacy and Safety of Ibuprofen plus Traction, Reposition, and Hip Spica Cast in the Treatment of Developmental Dysplasia of the Hip

Wiedemann–Steiner Syndrome: Case Report and Review of Literature

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