Segmental Dilatation of Intestine: A Case Report and Review of the Literature

Abstract

Segmental dilatation of intestine (SDI) is a rare disorder that leads to functional obstruction without stenosis and normally functioning ganglion cells. The etiology of the disease is unknown. Definitive treatment consists of segmental resection of the dilated segment with end-to-end anastomosis.

Segmental dilatation of the intestine

“…However, most authors are rather inclined to an embryological theory incriminating an extrinsic intrauterine intestinal compression (theory of Irving and Lister) [4][5][6]. The intestine can be strangulated at both its ends by the umbilical ring or other structures such as vitelline vessels or omphalomesenteric bands.…”

Congenital segmental dilatation of the duodenum: Report of a case

“…1 According to review articles, segmental intestinal dilatation is localized mainly in the ileum and colon, occasionally in the jejunum, and exceptionally in the duodenum. [4][5][6] To our knowledge, only three previous cases of duodenal segmental dilatation have been reported in the English literature. The origin of this condition remains unclear, but several etiologic theories have been proposed.…”

“…4 However, in duodenal dilatation, anatomic characteristics make it diffi cult to perform the usual resection techniques. The three previous cases were treated in the following way: partial resection with duodenal modeling in one; resection of the 3rd-4th portions with modeling of the 1st-2nd portions, side-to-end duodenojejunal anastomosis, and gastrojejunostomy in one; 3 and excision of the entire dilated duodenum leaving a sleeve of the duodenum around the ampulla in one.…”

Segmental dilatation of the ileum accompanying hypoproteinemia

“…Slightly more than 100 cases have been reported, of being greater majority ileal and colonic SIDs [2][3][4]. Jejunal and duodenal SIDs are seen less frequently [2,4,5].…”

“…It was suggested that in cases with omphalocele, some kind of vascular accident during fetal life induced the situation [5]. Irwing [9] postulated that the existence of an omphalocele was not necessary for the vascular insult, and entrapment of the intestines could have been occurred by the compression of the umbilical ring during the early stage of development.…”