Secundum atrial septal defect with Eisenmenger syndrome: A scarcely reported disease in Nigeria

Nwosu, Nneka; Omejua, Emeka G; Udora, Nneka; Nwosu, Ezinne

doi:10.4103/0300-1652.219346

Cited by 2 publications

(1 citation statement)

References 8 publications

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“…The left-toright shunt, therefore, transforms into a right-to-left shunt. This occurs when the pulmonary pressure and pressure in the right side of the heart reach the systemic pressure and pressure in the left side of the heart [10]. The result is severe cyanosis, even at rest.…”

Section: Discussionmentioning

confidence: 99%

Cardiac CT and Transesophageal Echocardiogram Evaluation of a Sinus Venosus-Type Atrial Septal Defect With Partial Anomalous Pulmonary Venous Return and a Persistent Left Superior Vena Cava

Mamatov¹,

Robinson²,

Sánchez³

2021

Cureus

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The sinus venosus (SV) plays a significant role in the embryological heart as the initial structure where the cardinal, umbilical, and vitelline veins drain before remodeling into the caval veins. As the human heart develops, the SV incorporates into the posterior wall of the right atrium. Sinus venosus atrial septal defects (SVASDs) result from a defect in the wall present among the right pulmonary veins, the superior vena cava (SVC), and the right atrium. Persistent left superior vena cava (PLSVC) occurs when the Marshall ligament does not regress, and in most cases, the PLSVC enters the coronary sinus before draining into the right atrium. Pulmonary hypertension from chronic left to right shunting makes recognizing this condition clinically significant. In this case report, both cardiac CT and transesophageal echocardiogram were used to further evaluate an SVASD with partial anomalous pulmonary venous return (PAPVR) of the right superior pulmonary vein, in addition to a PLSVC. The incidence of the co-occurrence of SVASD and PLSVC, as well as the association between the two, were discussed in this case report. Future research should focus on the potential genetic causes of this co-occurrence. It should also focus on patient treatment and outcomes at different stages of presentation to optimize patient management and improve mortality.

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Section: Discussionmentioning

confidence: 99%