Pulmonary sequestration is a rare malformation of the pulmonary parenchyma. Although pulmonary sequestration is rare finding but should be considered in patients with repeated episodes of bleeding. We describe a case of intralobar pulmonary sequestration found in a 27-year-old man admitted with massive hemoptysis and cough. He underwent lobectomy and achieved an excellent outcome. According to the potentially severe complications that they may cause, pulmonary sequestration should be removed whenever it is diagnosed; besides that repeated episodes of hemoptysis should be evaluated by more precise techniques such as ct angiography rather than broncoscopy.