Sclerosing Epithelioid Fibrosarcoma

Warmke, Laura M; Yu, Wendong; Meis, Jeanne M.

doi:10.1016/j.path.2023.06.009

Cited by 3 publications

(1 citation statement)

References 73 publications

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“…4 IPEH arises more commonly within a dilated vein than in an artery; however, it can also arise in varices, hemorrhoids, existing vascular tumors, and in hematomas. 18 IPEH consists of an intravascular proliferation of numerous papillae with a core of connective tissue and an endothelial surface within distended veins. 13 Our case had similar histologic features in both pulmonary arteries and veins.…”

Section: Intravascular Papillary Endothelial Hyperplasia In the Lungs...mentioning

confidence: 99%

Intravascular papillary endothelial hyperplasia in the lungs of a wild Korean raccoon dog

Tangchang,

Park,

Jung

et al. 2023

J VET Diagn Invest

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A male Korean raccoon dog of unknown age was rescued and placed at the Daejeon Wildlife Rescue Center, Korea. Physical examination revealed severe emaciation and dehydration, as well as thick crusts and alopecia over most of the body. During medical care, the animal died and was submitted for postmortem examination. Firm, brown-red lesions of various sizes were observed on the surface of the lungs. In cross-sections of the lungs, pulmonary vessels were thickened and dilated, with white irregular papillary luminal projections. Histologically, pulmonary blood vessels were severely hyperplastic, characterized by thickened dilated walls and fibrous papillary projections covered with a single layer of endothelial cells (ECs). Hyperplastic fibrous connective tissue was confirmed by Masson trichrome staining. The ECs expressed CD31. We diagnosed the lesion as intravascular papillary endothelial hyperplasia, a unique non-neoplastic reactive process that has not been reported previously in pulmonary vessels of canids, equids, or felids, to our knowledge.

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Section: Intravascular Papillary Endothelial Hyperplasia In the Lungs...mentioning

confidence: 99%

Intravascular papillary endothelial hyperplasia in the lungs of a wild Korean raccoon dog

Tangchang,

Park,

Jung

et al. 2023

J VET Diagn Invest

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Sclerosing epithelioid fibrosarcoma: a new mesenchymal non-meningothelial tumor involving the central nervous system?

Wolf,

Sinnes,

Reita

et al. 2024

Virchows Arch

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Sclerosing epithelioid fibrosarcoma of the pancreas: A case report

Sun,

Guo,

You

et al. 2024

World J Clin Cases

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BACKGROUND A sclerosing epithelioid fibrosarcoma (SEF) is a rare malignant fibroblastic soft tissue tumor that rarely occurs in intra-abdominal organs. A case of a SEF in the pancreatic head is reported herein, including its clinical manifestations, preoperative imaging features, gross specimen and pathological findings. CASE SUMMARY A 33-year-old male patient was admitted to Peking Union Medical College Hospital in December 2023 due to a one-year history of intermittent upper abdominal pain and the discovery of a pancreatic mass. The patient underwent an enhanced computed tomography scan of the abdomen, which revealed a well-defined, round mass with clear borders and calcifications in the pancreatic head. The mass exhibited progressive, uneven mild enhancement, measuring approximately 6.6 cm × 6.3 cm. The patient underwent laparoscopic pylorus-preserving pancreaticoduodenectomy. Postoperative pathological examination revealed that the lesion was consistent with a SEF. At the 3-month postoperative follow-up, the patient did not report any short-term complications, and there were no signs of tumor recurrence. CONCLUSION SEFs are rare malignant fibrous soft tissue tumors. SEFs rarely develop in the pancreas, and its preoperative diagnosis depends on imaging findings, with confirmation depending on pathological examination and immunohistochemistry. Currently, only four cases of pancreatic SEF have been reported in studies written in English. This case is the first reported case of a pancreatic SEF by a clinical physician.

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Sclerosing Epithelioid Fibrosarcoma

Cited by 3 publications

References 73 publications

Intravascular papillary endothelial hyperplasia in the lungs of a wild Korean raccoon dog

Intravascular papillary endothelial hyperplasia in the lungs of a wild Korean raccoon dog

Sclerosing epithelioid fibrosarcoma: a new mesenchymal non-meningothelial tumor involving the central nervous system?

Sclerosing epithelioid fibrosarcoma of the pancreas: A case report

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