1999
DOI: 10.1001/archderm.135.1.91
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Satoyoshi Syndrome

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Cited by 14 publications
(27 citation statements)
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“…Although the etiology remains unidentified, most authors believe that Satoyoshi syndrome may have an autoimmune basis. Laboratory findings often show presence of circulating antinuclear antibodies in many cases . Hypergammaglobulinemia was described in one patient .…”
Section: Pathogenesismentioning
confidence: 95%
See 1 more Smart Citation
“…Although the etiology remains unidentified, most authors believe that Satoyoshi syndrome may have an autoimmune basis. Laboratory findings often show presence of circulating antinuclear antibodies in many cases . Hypergammaglobulinemia was described in one patient .…”
Section: Pathogenesismentioning
confidence: 95%
“…Growth retardation was observed in 27% of ANA‐positive versus 86% of ANA‐negative, what can be attributed to the lower age of disease onset in ANA‐negative patients. In all ANA‐positive patients, a decrease in number and frequency of muscle spasms, improvement in diarrhea and partial (temporary) or full hair regrowth was observed after introduction of systemic glucocorticosteroid therapy …”
Section: Coexisting Diseasesmentioning
confidence: 99%
“…Skin biopsies were performed in two previously reported patients with childhood-onset Satoyoshi syndrome (9, 11). The histological findings of the skin were normal in one patient (9), while the other patient exhibited lymphocyte infiltration in the peribulbar area of the deep dermis (11). In contrast, the lymphocyte infiltration had spread to the papillary layer from the reticular layer in the dermis of the pigmented skin in our patient.…”
Section: Discussionmentioning
confidence: 54%
“…Other clinical findings include low levels of serum protein and total cholesterol (2), and endocrine disturbances, such as amenorrhea with a tendency toward the development of a hypoplastic uterus and ovaries (1). Complications of autoimmune diseases, such as myasthenia gravis (5) as well as the presence of autoantibodies (auto-Abs) (2,(6)(7)(8)(9)(10)(11) and responsiveness to treatment with corticosteroids (9,(11)(12)(13) and intravenous immunoglobulin (IVIG), have been reported in patients with Satoyoshi syndrome (7,14), indicating that an autoimmune mechanism may play a role in the onset of this syndrome, although the precise underlying mechanism remain unknown. The age of onset of Satoyoshi syndrome ranges from 5 to 19 years, with a mean age of 11 years (2, 15); however, adult-onset Satoyoshi syndrome is rare, having so far been reported in only a few patients (2,7,(15)(16)(17).…”
Section: Introductionmentioning
confidence: 99%
“…Se han utilizado para tratarlos, dantrolen, benzodiacepínicos, anticonvulsivantes y toxina botulínica 2,12 con resultados variables y que no están enfocados a la patogenia de la enfermedad. Desde los años noventa la mayoría de los pacientes con síndrome de Satoyoshi se han beneficiado del tratamiento con corticoides que se ha mantenido por más de un año 5,11 , con una significativa reducción de los espasmos musculares, revirtiendo la caída del cabello y logrando el inicio de la menstruación en algunos casos de mujeres afectadas 5,[7][8][9]11,15,[17][18][19][20] . También se han utilizado inmunosupresores como metotrexato, tacrolimus e inmunoglobulinas 9,11 que pueden ser alternativas útiles cuando las dosis de esteroides necesarias para revertir los síntomas ocasionan efectos adversos indeseables o respuesta parcial.…”
Section: Discussionunclassified