Sarcome d’Ewing primitif de la voûte du crâne

Bricha, M.; Jroundi, L.; Boujida, N.; Hassani, M.R. El; Chakir, N.; Jiddane, M.

doi:10.1016/s0221-0363(07)78370-1

Cited by 9 publications

(5 citation statements)

References 4 publications

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“…Removal of the involved bone is to be done. [ 8 30 ] The primary treatment consists of neoadjuvant systemic CT, with a combination of vincristine, doxorubicin, and cyclophosphamide, alternating with ifosfamide and etoposide, given for 12–24 weeks. This is followed by definitive local treatment of surgery or radiation, or surgery and postoperative radiation directed at the primary site.…”

Section: Discussion and Review Of Literaturementioning

confidence: 99%

Primary intracranial dural-based Ewing sarcoma/peripheral primitive neuroectodermal tumor mimicking a meningioma: A rare tumor with review of literature

et al. 2017

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Ewing sarcoma/peripheral primitive neuroectodermal tumor (ES/pPNET) is a malignant small, round cell tumor arising from bone and soft tissue in children and young adults. It can occur at osseous and extraosseous sites. Its usual locations are diaphysis of long bones followed by pelvis, ribs, vertebrae, and rarely skull. We reviewed the literature and PubMed advanced search on ES/pPNET occurring at extraosseous sites, mainly involving the central nervous system (CNS). We reported a case of a 22-year-old male presenting with seizure finally diagnosed as a case of ES/pPNET. The challenges in management of this rare CNS tumor and its differential diagnosis are highlighted. We found that most cases of ES involving CNS represent secondary metastases from extracranial sites of ES/pPNET and there are rare case reports of primary intracranial ES-pPNET. Furthermore, among these intracranial tumors, most common tumors occupy an intraaxial location and only a handful of cases of dural-based or extraaxial tumors mimicking meningioma are reported. Differentiation of pPNET from central PNET (cPNET) is important as it has definitive therapeutic and prognostic implications. Awareness of this entity of ES/pPNET, its rare dural presentation, and differentiation from the more common cPNET is needed for appropriate patient management. Meningeal ES/pPNET has to be kept in mind in the differential diagnosis of meningeal tumors eroding bone.

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Section: Discussion and Review Of Literaturementioning

confidence: 99%

Primary intracranial dural-based Ewing sarcoma/peripheral primitive neuroectodermal tumor mimicking a meningioma: A rare tumor with review of literature

et al. 2017

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“…[ 23 ] Among the 8 previous cases of primary calvarial Ewing's sarcoma that involved extracranial extension, osteolytic destruction or cortical violation was observed in 7 cases; the remaining case was a congenital case in which Ewing's sarcoma occurred in the frontonasal area. [ 2 5 8 11 13 15 16 25 ] Although a sunburst periosteal reaction was observed in the present case, osteolytic lesions, honeycomb lesions, bone expansion, and cortical violation were not observed on the skull X-ray or CT [Figure 1a , b ]. F-18 FDG PET/CT showed a strongly labeled tumor on the surface of the nonlabeled temporal bone [ Figure 1c ].…”

Section: Discussionmentioning

confidence: 70%

Primary pericranial Ewing′s sarcoma on the temporal bone: A case report

et al. 2016

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Background:Primary Ewing's sarcoma originating in the pericranium is an extremely rare disease entity.Case Description:A 9-year-old female patient was admitted to our department due to a left temporal subcutaneous mass. The mass was localized under the left temporal muscle and attached to the surface of the temporal bone. Head computed tomography revealed a mass with bony spicule formation on the temporal bone, however, it did not show bone destruction or intracranial invasion. F-18 fluorodeoxyglucose positron emission tomography showed no lesions other than the mass on the temporal bone. Magnetic resonance imaging showed that the mass was located between the temporal bone and the pericranium. The mass was completely resected with the underlying temporal bone and the overlying deep layer of temporal muscle, and was diagnosed as primary Ewing's sarcoma. Because the tumor was located in the subpericranium, we created a new classification, “pericranial Ewing's sarcoma,” and diagnosed the present tumor as pericranial Ewing's sarcoma.Conclusion:We herein present an extremely rare case of primary pericranial Ewing's sarcoma that developed on the temporal bone.

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“…What is already known is that, when located within the skull (less than 1% of cases), [4814] these tumors tend to pass the cortical of the bone of origin to spread into the adjacent soft tissues [33] but in such reported presentations, dural break through was associated with diffuse massive epidural masses [1721] responsible of what so called volcano-shape radiological feature. [17]…”

Section: Discussionmentioning

confidence: 99%

“…Generally the tumor presents with features of raised intracranial pressure as well as focal neurological deficits [481426] and the imaging characteristics of this rare tumor in an extra-axial location consists of high attenuation on CT, which can show the intracranial or extra cranial extension of the tumor as well as even slight bone destruction. [2437] MRI will show low signal intensity on T2-weighted sequences, [24] which usually suggest hyper cellularity, well known in this category of tumors and by providing multiplanar views it will also demonstrate the tumor extent, which is of great help in surgical planning.…”

Section: Discussionmentioning

confidence: 99%

Dural metastasis of Ewing′s sarcoma

Nsir

Boughamoura²,

Maatouk³

et al. 2013

Surg Neurol Int

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Background:Metastatic Ewing’s sarcoma to the central nervous system is an uncommon condition and debate concerning the true origin of its metastases is still up to date. To the best of our knowledge, only two cases of dural metastatic Ewing’s sarcoma have been published in the English medical literature. We present an additional case in a 24-year-old female and discuss the pathogenesis of these unusual tumors with review of the relevant literature concerning their treatment and outcome.Case Description:A 24-year-old female with previous history of pelvis Ewing’s sarcoma and recently discovered lung metastases, presented with moderate headache for the past 2 weeks and weakness in her left leg for the past 2 days. Computed tomography scan and magnetic resonance imaging revealed an extra-axial right frontoparietal mass invading the superior sagittal sinus but with clear delineation with brain parenchyma. Imaging features were suggestive of a meningioma as no abnormalities in the skull abutting to the tumor were noted. The patient underwent surgical removal of her tumor. Near total resection was achieved and histological examination showed evidence of metastatic Ewing’s sarcoma. Postoperative adjuvant radiation and chemotherapy were administered. The patient improved well postoperatively with full recovery of her motor weakness. She is symptom free with no signs of progression, at most recent follow-up, 8 months after surgery.Conclusion:Despite its rarity, metastatic Ewing’s sarcoma must be considered in the differential diagnosis of extra-axial dural masses particularly meningiomas.

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Sarcome d’Ewing primitif de la voûte du crâne

Cited by 9 publications

References 4 publications

Primary intracranial dural-based Ewing sarcoma/peripheral primitive neuroectodermal tumor mimicking a meningioma: A rare tumor with review of literature

Primary intracranial dural-based Ewing sarcoma/peripheral primitive neuroectodermal tumor mimicking a meningioma: A rare tumor with review of literature

Primary pericranial Ewing′s sarcoma on the temporal bone: A case report

Dural metastasis of Ewing′s sarcoma

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