“…This tumor develops predominantly in the sacrococcygeal (50%), spheno-occipital (35%) and cervical (15%) region and is generally regarded as a locally aggressive tumor with slow progression growth rate and metastatic incidence ranging from 5 to 40% [5,20]. Its incidence is highest in the sixth decade, but it can also be found in younger population, even infancy (1%) [3,4,12,26]. The male-female ratio among patients is 1.8-2.1.…”