Ross-Konno Procedure With Cylinder Mitral Valve Replacement in 49 Days Old Infant

Abstract

A neonate with antenatally diagnosed severe aortic valve stenosis, left ventricular outflow tract obstruction, left ventricular endocardial fibroelastosis, and severe mixed mitral valve disease was admitted to our center for balloon aortic valvuloplasty. On day 49, we performed a Ross-Konno procedure and mitral valve replacement on the baby, whose weight was 3.4 kg. Right ventricle-to-pulmonary artery continuity was restored with a handmade trileaflet Gore-Tex conduit. We used a handmade cylindrical prosthesis made from decellularized equine pericardium in the mitral position. We observed improvement in left ventricular function and good performance of aortic, pulmonary, and mitral prostheses at four months of follow-up.

Creation of a Neo-Mitral Valve With Right Atrial Appendage Tissue in an Infant

“…They can be constructed to any size and are not rigid. Previously, CorMatrix or bovine or equine pericardium has been used to construct the “cylinder valve,” 1,2,6 although the lack of regenerative potential and possibility of inflammatory reaction have been recognized. We decided to use the RAA due to our previous experience with using it as a pulmonary valve substitute 5,7 as well as partial aortic valve reconstruction.…”

“…Handmade cylinder valves created using CorMatrix (CorMatrix: porcine small intestinal submucosa) or decellularized xenograft pericardium have been used in the tricuspid and mitral positions. 1,2…”

“…Handmade cylinder valves created using CorMatrix (CorMatrix: porcine small intestinal submucosa) or decellularized xenograft pericardium have been used in the tricuspid and mitral positions. 1,2 Case Report A 3.3 kg infant with aortic arch hypoplasia and muscular ventricular septal defect (VSD) underwent repair on day of life 10. Preoperative echo findings showed a 6.5-mm mitral valve (MV) annulus (z score −3).…”