Rosai-Dorfman Disease Presenting as Isolated Subglottic Mass- an Extremely Rare Presentation

Vats, Deepa

doi:10.15406/jlprr.2016.03.00087

Search citation statements

Order By: Relevance

Paper Sections

Select...

Discussion1

Citation Types

Supporting

Mentioning

Contrasting

Year Published

2018

Publication Types

Select...

Article1

Relationship

Self Cite0

Independent1

Authors

Journals

Cited by 1 publication

(1 citation statement)

References 5 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…Histological hallmarks of the disease include emperipolesis, positive immunohistochemical staining with S100 protein and CD68, and negative staining with CD1a. 1,2,6,7 Our case was S100-positive. Management of tracheobronchial RDD depends on the presentation.…”

Section: Discussionmentioning

confidence: 53%

Rosai-Dorfman disease of the trachea: an extremely rare benign tumor

Santosham¹,

Jacob

Phadke³

et al. 2018

Asian Cardiovasc Thorac Ann

View full text Add to dashboard Cite

Rosai-Dorfman disease or sinus histiocytosis is a nonmalignant disease chiefly presenting as a painless cervical lymphadenopathy, although extranodal involvement is also frequent. Involvement of the tracheobronchial tree is extremely rare, and there are no clear guidelines on management. Rosai-Dorfman disease usually presents as a tracheal tumor, although it may also present with extraluminal compression. Only 12 cases have been reported in the English language literature. Histopathology is required to confirm the diagnosis. We describe what we think is India’s first reported case of histologically proven tracheal Rosai-Dorfman disease in a 40-year-old otherwise healthy lady.

show abstract