Right aortic arch with isolation of the left innominate artery in a case of double chamber right ventricle and ventricular septal defect

Abstract

Herein, we report an unusual case of right aortic arch with isolation of the left innominate artery in a case of double chamber right ventricle with ventricular septal defect. The blood supply to the innominate artery was by a collateral arising from the descending aorta. The embryological development of this anomaly can be explained by the hypothetical double aortic arch model proposed by Edwards with interruption of the arch at two levels.

Right aortic arch with mirror image branching pattern and isolated left brachiocephalic artery: A case report

“…The first case of a right aortic arch with an ILBA was described by D'Cruz and Levine et al, in 1966 [13] . Since then cases have been reported where vertebrobasilar insufficiency was clinically observed [13] .…”

“…The first case of a right aortic arch with an ILBA was described by D'Cruz and Levine et al, in 1966 [13] . Since then cases have been reported where vertebrobasilar insufficiency was clinically observed [13] . Patients with right sided aortic arch and ILBA are prone to vertebrobasilar insufficiency secondary to subclavian artery steal phenomenon [11] .…”

“…Multimodality imaging evaluation has been used to help detection and categorization of aortic arch abnormalities [13] . These modalities include echocardiography, computed tomography angiography, cardiac computed tomography, cardiac magnetic resonance and magnetic resonance angiography [10] .…”

Isolated left brachiocephalic artery with the right aortic arch

“…[45] Even in these cases, the anomaly was not isolated, albeit associated with intracardiac defects such as ventricular septal defect and pulmonary stenosis. Association of this arch anomaly with DiGeorge syndrome[4] and Down syndrome is also reported.…”

Isolation of Left Subclavian Artery with Tetralogy of Fallot—A Case Report

“…It is the least common type of RAA, occurring in 0.8% of a series of 298 RAA, reported by Stewart and associates [2] [3]. The embryological development of such a malformation can be explained by using the concept of "hypothetical double aortic arch plan" first given by Edwards in 1948 [4] [5]. There is interruption of the aortic arch at two levels, one between the left common carotid artery and the LSCA, and the second between the left ductus arteriosus and the aortic root.…”