Right aortic arch with isolated left brachiocephalic artery

Incomplete isolation of the left innominate artery from the right aortic arch: a rare case of double-outlet right ventricle with pulmonary stenosis

“…2 We postulated that our patient had a right aortic arch with mirror-image branching with the exceptions of the incompletely regressed left branch of aortic sac and left patent ductus arteriosus. There are several case reports of isolated left innominate artery due to the interruption of the left branch of the aortic sac 3,4,5,6,7 ; however, to the best of our knowledge, there is only one case report on incomplete isolation of the left innominate artery. 8 In our patient, pulmonary stenosis worsened over time in the setting of aggravating right ventricular outflow obstruction; the pulmonary blood flow was solely delivered via the left carotid artery and the narrow connection between the ascending aorta and the left innominate artery when she underwent surgery.…”

Agenesis of the Left Internal Carotid Artery in the Right Aortic Arch with Isolation of the Left Innominate Artery Associated with Ruptured Cerebral Aneurysm: Case Report

“…It is unusual for patients to have this condition in adulthood without coexisting congenital cardiac anomalies; the association of a patent ductus arteriosus or other cardiac abnormalities, resulting in cardiovascular dysfunction, has been reported in neonates and in early life. [2][3][4] Agenesis of the ICA is also a rare congenital anomaly; it has been documented in less than 0.01% of the population. 5) Although a few instances of both aortic arch anomaly and agenesis of the ICA have been reported, 6) ours is the first documentation of this type of complex anomaly and no patients with additional dysplasia of the posterior circulation have appeared in the literature.…”

“…3,4) ICA agenesis involves the abnormal regression, involution, or atresia of the third aortic arches and dorsal aorta; the pathogenesis of dysplasia of the posterior circulation remains unknown. The basilar artery distal to the primitive trigeminal artery derives from the ipsilateral ICA and anastomoses with the vertebrobasilar system.…”

Unmasking of an isolated right subclavian artery from the pulmonary artery after device occlusion of a patent arterial duct

“…The only management option to address an isolated subclavian artery and maintain normal prograde flow is surgical implantation to either the carotid artery or the aortic arch directly via direct anastomosis or a bypass graft . Other surgical options generally include ligation of the RSCA or to ligate the connecting artery to the right pulmonary artery to avoid/prevent SAS.…”