Rhabdomyoma and Ventricular Preexcitation Syndrome

Pre‐excitation syndrome secondary to cardiac rhabdomyomas in tuberous sclerosis

“…11 The accessory pathway identified on the surface ECG tends to correlate with the location of the tumours. 12,13 The 12‐lead ECG in this patient suggested that the accessory pathway was left sided and this was concordant with the position of the tumour straddling the left atrioventricular groove. Ventricular pre‐excitation has also been found in association with rhabdomyomas.…”

Cardiovascular Manifestations of Tuberous Sclerosis Complex and Summary of the Revised Diagnostic Criteria and Surveillance and Management Recommendations From the International Tuberous Sclerosis Consensus Group

“…38–42 Ventricular preexcitation associated with abnormal AV connections has also been commonly reported and has been noted to participate in rapid potentially life‐threatening anomalous AV conduction during atrial fibrillation. 43–45 The mechanisms of arrhythmia have often been directly linked to the location of specific cardiac rhabdomyomas. 46 Indeed, abnormal AV connections associated with TSC have been shown histologically to be directly related to rhabdomyomas tumor tissue connecting the atrium to the ventricle, rather than a “typical” accessory pathway.…”

Congenital giant cardiac tumor with severe left-ventricular inflow and outflow obstruction and arrhythmia treated with pulmonary artery banding and long-term amiodarone infusion

“…SVT and ventricular pre-excitation syndrome associated with rhabdomyoma had been previously documented. [5] The previous report suggests cardiac tumor itself works as macroscopic or microscopic accessory connection. SVT in this case was drug-resistant and caused hemodynamic instability.…”

“…Sometimes it is complicated by severe obstruction of inflow or outflow of the ventricular tract leading to heart failure[1–3] and arrhythmia such as supraventricular or ventricular tachycardia (SVT or VT)[45] and bradycardia due to conduction disturbance. Management for such cases is very difficult.…”