Retroperitoneal Malignant Fibrous Histiocytoma

Abstract

We present 2 cases of malignant fibrous histiocytoma (MFH) of the retroperitoneum. Only 12-14% of all MFH occur in the retroperitoneum. Both patients were operated with the diagnosis of a kidney tumor. The surgical exposure showed a tumor arising from the retroperitoneum, infiltrating or surrounding the kidney. We would like to emphasize that large tumors of the retroperitoneum which resemble kidney tumors can also arise from mesen-chymal tissue.

Primary Renal Malignant Fibrous Histiocytoma

“…Infrequent primary localizations include the urinary bladder, prostate, spermatic cords and kidneys [1,5,7]. Primary malignant fibrous histiocytoma of the kidney is an unusual presentation with only 22 cases reported to date [5,6,8]. Our report adds 1 further case as a contribution to familiarity with the entity, including preoperative diagnosis, pathologic differential diagnosis, specific therapy and prognosis.…”

“…Our report adds 1 further case as a contribution to familiarity with the entity, including preoperative diagnosis, pathologic differential diagnosis, specific therapy and prognosis. Age predilection lies between the 5th and 7th decades with occurrence in children and young adults rare [2][3][4]8].…”