“…As the name implies, RPF presents with a grayish-white fibrous plaque, more dense in the midline, usually at the bifur cation of the aorta [Hem and Mathisen, 1984], The idio pathic form of the disesae appears usually in men of late middle age with back pain, renal impairment and not rarely with anuria [Deane et al, 1983], An autoimmune mechanism seems to be of prime importance in the pathogenesis of the disease [Wagenknecht and Hardy, 1981], although genetic or familial factors have recently been incriminated [Duffy et al, 1984], The selection of a therapeutic strategy remains controversial. The proce dures recommended by the different centers vary from corticosteroids alone [Morandi and Grob, 1971 ;Ross and Goldsmith, 1971;Ochsner et al, 1975] to ureterolysis and/or to autotransplantation [Palleschi and McAninch, Patients and Methods During the last 12 years, 11 cases (8 male) were diagnosed as having idiopathic RPF (IRPF).…”