Retinal Detachment in a 40-Year-Old Man With Sturge-Weber Syndrome

Chiou, Carolina A.; Gragoudas, Evangelos S.

doi:10.1001/jamaophthalmol.2020.4665

Cited by 2 publications

(2 citation statements)

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“…A history of prior retinal detachment was treated with proton beam therapy 7 years ago, while recurrent retinal detachment was treated with acetazolamide administration and a posterior sclerectomy surgery. [5] Treatment of serous retinal detachment must address the underlying local or systemic disease which in this case choroidal haemangioma has been a major causes. [6] Conventional therapy includes photodynamic therapy, external beam radiation therapy, and oral propranolol.…”

Section: Discussionmentioning

confidence: 99%

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Posterior sclerectomy for persistent serous retinal detachment with secondary glaucoma in Sturge–Weber syndrome: A case report

Nurtania,

Kiuchi,

Muhlisah

et al. 2023

Medicine

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Introduction: A serous retinal detachment is one of the most likely ocular manifestation of Sturge-Weber syndrome (SWS). This finding can frequently occur as a complication after filtering surgery to maintain the intraocular pressure (IOP). Proper treatment has been approached with choroidal hemangioma as an organ target. To the best of our knowledge, various treatments for SRD are associated with diffuse choroidal hemangioma has been approached. However, a second retinal detachment following radiation therapy has worsened the situation. Here, we report an unexpected serous retina and choroidal detachment after non penetrating trabeculectomy. Although radiation therapy has been proposed for previous detachment to the ipsilateral eye in this case, repetition radiation therapy was not suggested concerning the health and quality of life especially in for young subjects. However, the kissing choroidal detachment in this case necessitated immediate intervention. Thus, posterior sclerectomy was performed for the recurrent retinal detachment. We believe that an intervention for a SWS case related complication will remain a significant and important to share as a public health contribution. Case presentation: A 20 year-old male confirmed with SWS with no known family history was diagnosed with SWS. He was gain from another hospital for glaucoma therapy. On the left brain MRI showed severe hemiatrophy in the frontal and parietal lobes and leptomeningeal angioma. Although his right (RE) eye had 3 gonio surgeries, 2 Baerveldt tube shunts and Micropulse trans-scleral cyclophotocoagulation, his IOP remained uncontrollable when he was 20 years old. RE IOP was in controlled after non-penetrating filtering surgery hence, his RE developed a recurrent serous retinal detachment. A posterior sclerectomy was performed in 1 quadrant of the globe to drain subretinal fluid. Conclusion: Sclerectomies to the inferotemporal quadrant of the globe for serous retinal detachment associated with SWS are considered efficient for optimal drain subretinal fluid, resulting in complete regression of detachment.

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Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%