Renal Rhabdomyosarcoma in a Young Woman with Gross Hematuria: A Case Report

Allameh, Farzad; Karkan, Morteza Fallah; Rakhshan, Azadeh

doi:10.5812/ijcm.10649

Cited by 6 publications

(7 citation statements)

References 9 publications

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“…The new World Health Organization (WHO) classification divides RMSs into four groups: alveolar RMA, embryonal RMA, spindle cell/sclerosing RMA, and pleomorphic RMA. Adult RMS begins in the major skeletal muscle [ 5 ]. It originates from the embryonic mesenchyme and has the potential to differentiate into rhabdoid muscle cells.…”

Section: Discussionmentioning

confidence: 99%

Retroperitoneal Spindle Cell Rhabdomyosarcoma With Compression Features in a 48-Year-Old Male: A Case Report

Ramesh¹,

Jangda²,

Annam³

et al. 2022

Cureus

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Spindle cell rhabdomyosarcoma (SC-RMS) is an unprecedented version of embryonal rhabdomyosarcomas (RMSs) that emerges from the mesenchyme with the capacity to differentiate into skeletal muscle cells. Retroperitoneal RMS is extremely rare in the adult population. We present the case of a primary spindle cell retroperitoneal RMS with compression features. Investigation-based diagnosis of RMS is difficult due to the lack of specificity of clinical findings. Radiology does not help in making an accurate diagnosis. Surgical removal of the tumor followed by chemotherapy and radiotherapy is the best possible treatment for RMS in adults. SC-RMS has a poor long-term prognosis. To our knowledge, such cases of retroperitoneal SC-RMS compressing the abdominal viscera and resulting in hydroureteronephrosis have never been reported before.

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Section: Discussionmentioning

confidence: 99%

Retroperitoneal Spindle Cell Rhabdomyosarcoma With Compression Features in a 48-Year-Old Male: A Case Report

Ramesh¹,

Jangda²,

Annam³

et al. 2022

Cureus

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“…In 2016, Lin et al reported an 18 year old patient discovered to have a pleomorphic-type primary renal RMS 9. Furthermore, in 2017, Farzad Allameh and colleagues published a case report of a 33-year-old woman who presented with gross haematuria and was later found to have the botryoid variant of RMS as a primary tumour of the kidney 4…”

Section: Discussionmentioning

confidence: 99%

“…Radiographically, primary renal RMS has characteristics similar to renal cell carcinoma with no predictive features on CT imaging. Thus, definitive diagnosis is dependent on postoperative immunohistochemical analysis after surgery 3 4. Grignon et al first established criteria necessary to make the diagnosis of primary sarcoma of the kidney.…”

Section: Introductionmentioning

confidence: 99%

Primary renal embryonal rhabdomyosarcoma in an adult patient

Connor

Tsui

et al. 2020

BMJ Case Rep

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Adult renal rhabdomyosarcoma (RMS) is a rare and aggressive entity with a paucity of data and reports in the literature. As a result, treatment guidelines for this malignancy are not well-established. Herein, we present the diagnosis, management and clinical course of a 39-year-old patient diagnosed with primary renal embryonal RMS (ERMS) following radical nephrectomy. We also review the existing literature on primary renal ERMS.

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“…Metanephric adenoma (MA) is a rare benign kidney tumor with an excellent prognosis (1). The most common part of the kidney involved in various benign or malignant tumors is the tubular epithelium (2). MA originates from epithelial cells, and because of its commonly unspecific clinical and radiological characteristics, it can be difficult to distinguish it from malignant neoplasms preoperatively (3,4).…”

Section: Introductionmentioning

confidence: 99%

Metanephric Adenoma: A Case Report of a Rare Benign Renal Tumor

et al. 2021

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Introduction: Metanephric adenoma (MA) is a rare benign kidney tumor with an excellent prognosis, which is usually diagnosed incidentally with no symptoms. The mean age of patients with MA is about 41 years, ranging from 5 months to 83 years in previous studies. Case Presentation: In this study, we present the case of a 29-year-old woman with a diagnosis of MA after nephrectomy. The ultrasound study showed a hyperechoic mass. The intravenous (IV) contrast-enhanced abdominopelvic computed tomography (CT) scan showed a hypodense mass. Based on the results of pathological features and immunohistochemistry (IHC) (positive vimentin, WT1, and PAX8), the diagnosis of MA was established. Conclusions: The diagnosis of MA is commonly based on pathological findings. Therefore, if MA is suspected, renal biopsy, partial nephrectomy, or follow-up of the patient can be used. However, further studies are needed to differentiate MA from papillary renal cell carcinoma and nephroblastoma before taking aggressive measures.

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Renal Rhabdomyosarcoma in a Young Woman with Gross Hematuria: A Case Report

Cited by 6 publications

References 9 publications

Retroperitoneal Spindle Cell Rhabdomyosarcoma With Compression Features in a 48-Year-Old Male: A Case Report

Retroperitoneal Spindle Cell Rhabdomyosarcoma With Compression Features in a 48-Year-Old Male: A Case Report

Primary renal embryonal rhabdomyosarcoma in an adult patient

Metanephric Adenoma: A Case Report of a Rare Benign Renal Tumor

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