“…In majority of cases, this condition is diagnosed incidentally but can present with flank mass, pain, hypertension, haematuria, chyluria, renal vein thrombosis, ureteral obstruction, lower limb oedema, ascites, pleural effusion or even chylothorax. [ 2 ] Similar to its aetiopathogenesis, to date, no consensus has been reached regarding its optimal management. Management includes conservative options such as follow-up when asymptomatic, aspiration with or without sclerotherapy or pigtail placement to more invasive options such as laparoscopic cyst deroofing, marsupialisation, excision or very rarely even nephrectomy.…”