Renal Dysgenesis and Cystic Disease of the Kidney

Pope, John C.

doi:10.1016/b978-1-4160-6911-9.00118-3

Cited by 8 publications

(16 citation statements)

References 306 publications

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“…The present meta-analysis was conducted to help address these questions. This analysis included 37 studies from 18 different countries, 12 of which were prospective (Table A. 1), and all but one of which were considered to be of moderate-to-high quality as per the MINORS tool [21]. It was found that of the 1800 patients who underwent VCUG, 17% had VUR in the contralateral kidney, and of those who had VUR, 41% had dilating VUR.…”

Section: Discussionmentioning

confidence: 99%

“…2). In three cases, the VUR grade was undefined because of megaureter (2) and infundibular stenosis (1). Pooled results for VUR were divided by grades, as well as by low versus high grades, and are summarized in Table 1.…”

Section: Primary Outcomedvurmentioning

confidence: 99%

“…Multicystic dysplastic kidneys (MCDKs) are the most common type of renal cystic disease and the second most common cause of an abdominal mass in infants [1]. MCDK can be familial, but most cases are sporadic [2].…”

Section: Introductionmentioning

confidence: 99%

See 2 more Smart Citations

A meta-analysis of the incidence and fate of contralateral vesicoureteral reflux in unilateral multicystic dysplastic kidney

Erlich

Lipsky

Braga

2019

Journal of Pediatric Urology

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Section: Discussionmentioning

confidence: 99%

Section: Primary Outcomedvurmentioning

confidence: 99%

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A meta-analysis of the incidence and fate of contralateral vesicoureteral reflux in unilateral multicystic dysplastic kidney

Erlich

Lipsky

Braga

2019

Journal of Pediatric Urology

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“…MSK is a rare renal congenital malformation characterized by a tubular dilatation of the distal portion of the collecting ducts, with numerous cysts and diverticula strictly confined to the medullary pyramids. 1 Generally it occurs bilaterally, being rare the unilateral form. This malformation causes nephrocalcinosis and recurrent calcium lithiasis secondary to the presence of hypercalciuria, hypocitraturia and distal renal tubular acidosis (dRTA) as long as there is urinary stasis in the dilated ducts.…”

Section: Discussionmentioning

confidence: 99%

Unilateral Medullary Sponge Kidney

Neira

Barrera

Astroza

2018

JELEU

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A 40-year-old female with an allergy to medium contrast, presented with bilateral loin pain and renal colic type radiation. Image study with non-contrast computerized tomography and magnetic resonance imaging revealed multiple nephrolithiasis and a complex cyst at lower pole of the right kidney and no findings in the left one. The patient was treated with laser lithotripsy by flexible ureterorenoscopy revealing multiple lithiasis within cystic dilatations of the urothelium. The complex cyst was submitted to partial nephrectomy. Finally, biopsy demonstrated that it was renal parenchyma with polycystic changes in the external corticomedullary area. All findings were compatible with unilateral medullary sponge kidney diagnosis.

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“…Incidence ranges from 1 in 30,000 to 1 in 50,000 individuals. It has over 95% penetrance by the age of 65 years in affected individuals [4]. The mean age at presentation is 35 to 40 years [5].…”

Section: Discussionmentioning

confidence: 99%

Adrenal Cortex-Sparing Surgery for Bilateral Multiple Pheochromocytomas in a Patient with Von Hippel-Lindau Disease

Esen

Acar

Tefekli̇

et al. 2012

Case Reports in Medicine

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Pheochromocytomas can be a part of familial neoplastic syndromes, in which case they tend to be multiple and involve both adrenal glands. Therefore, sparing adrenocortical function represents a major concern while dealing with these hereditary lesions. Herein, we describe the clinical characteristics and the management strategy of a patient with von Hippel-Lindau (VHL) disease who had multiple, bilateral pheochromocytomas as well as bilateral renal masses, pancreatic masses, and a paracaval mass. Only a portion of the left adrenal gland has remained in situ after two consecutive open surgeries and a percutaneous radiofrequency ablation which have been performed to treat the various components of this syndrome. No adrenal or extra-adrenal pheochromocytoma recurrences have been detected during a follow-up period of more than 2 years. Pancreatic and adrenal functions were normal throughout the postoperative period and never necessitated any replacement therapy. Adrenal cortex-sparing surgery is a valid option for VHL disease patients who present with synchronous bilateral adrenal pheochromocytomas.

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Renal Dysgenesis and Cystic Disease of the Kidney

Cited by 8 publications

References 306 publications

A meta-analysis of the incidence and fate of contralateral vesicoureteral reflux in unilateral multicystic dysplastic kidney

A meta-analysis of the incidence and fate of contralateral vesicoureteral reflux in unilateral multicystic dysplastic kidney

Unilateral Medullary Sponge Kidney

Adrenal Cortex-Sparing Surgery for Bilateral Multiple Pheochromocytomas in a Patient with Von Hippel-Lindau Disease

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