Remimazolam Anesthesia for a Pediatric Patient With Glutaric Aciduria Type I: A Case Report
Tomoko Tsuruno,
Hiroki Tateiwa,
Yuki Hashimoto
et al.
Abstract:Glutaric aciduria type I (GA-1) is a rare metabolic disorder caused by an autosomal, recessive, inherited deficiency of glutaryl-CoA dehydrogenase. Reports on the anesthetic management of patients with GA-1 are limited. It has been suggested that inhalation anesthesia is safer than propofol due to the mitochondrial dysfunction inherent in GA-1. However, inhalation anesthesia poses a risk, albeit rare, of malignant hyperthermia, which can result in severe neurological damage in GA-1 patients. Therefore, we cons… Show more
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