Rehabilitation in Franceschetti Syndrome: An Interdisciplinary Approach Using Bone-Anchored Hearing Aids

A Systematic Review of the Nonacoustic Benefits of Bone-Anchored Hearing Aids

“…First, search strings were derived and submit- Mylanus et al (1995) Yes No Yes Mylanus et al (1998) Yes No Yes Niparko et al (2003) Yes No Yes Reuter et al (1997) No No No Snik et al (1998) Yes No Yes Snik et al (1992) Yes No Yes Snik et al (1994) Yes No Yes Snik et al (1995) Yes No Yes Stenfelt et al (2000) Yes No Yes Tjellstrom et al (1995) Yes ted to the databases to identify lists of potential articles. Second, three reviewers inspected the lists of retrieved articles for relevant titles and excluded those that were clearly not on the topic (e.g., oncology treatments or pediatric focus), with 90% interjudge reliability.…”

“…A table entry of "yes" indicates that the study met the specific inclusion criterion; an entry of "no" indicates that the study did not, resulting in exclusion from the systematic review. The vast majority of the studies were excluded because they failed to use either generic health-related or disease-specific QOL outcome measures, such as those involving pediatric patients in a case study format (Reuter, Marks, Jovanovic, et al, 1997). Table 3 provides the details for the studies that were included for analysis.…”

Bilateral Bone‐Anchored Hearing Aids for Bilateral Permanent Conductive Hearing Loss

“…15,16 Outcomes were presumably assessed by the study investigators (this information was not stated) in all studies. Quality assessment scores ranged from 2 to 6 out of 7 ( Table 1).…”

“…19 Comparisons were intra-subject or with a control group in 8 studies. [16][17][18][19][20][21][22]25 All studies used validated methods of assessment. One study included a power calculation for determination of adequate sample size.…”

Fully implantable hearing device as a new treatment of conductive hearing loss in Franceschetti syndrome

“…In Franceschetti (a.k.a Treacher Collins) syndrome with bilateral external ear canal agenesis, conventional acoustic hearing aids cannot be used. In this case, a boneanchored hearing aid (BAHA) is one option [2]. However, BAHA implants have the inherent psychological and biological disadvantages of open implants with risks of local inflammation.…”