RE: Successful management of hereditary angioedema with normal C1-INH (type III HAE) when using on-demand ecallantide

Cronin, Julia A.; Minto, Heather; Maples, Kathryn T.

doi:10.1016/j.jaip.2013.11.016

Cited by 3 publications

(2 citation statements)

References 6 publications

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“…Ecallantide is another agent used to treat acute attacks. It is a plasma-kallikrein inhibitor which has been used to treat acute attacks of HAE with normal C1-INH with some success 31 32. C1-INH concentrate is another agent that has been used; however, its efficacy is debatable.…”

Section: Discussionmentioning

confidence: 99%

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Wolf in the sheep’s clothing: intestinal angioedema mimicking infectious colitis

et al. 2018

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Hereditary angioedema (HAE) is a relatively rare clinical entity that can potentially cause life-threatening airway or intestinal oedema, patients with the latter usually presents with symptoms of gastroenteritis like vomiting, diarrhoea and abdominal pain. Here, we present a unique case of a less recognised type of HAE that is type III in a patient who presented with signs and symptoms consistent with infectious colitis. She previously had similar episodes and was managed multiple times with antibiotics, with no satisfactory response. There, she underwent extensive diagnostic evaluation. On the basis of findings of further investigations on the current visit, she was eventually diagnosed with intestinal angioedema. To the best of our knowledge, the present paper represents the third reported case of type III HAE-induced intestinal angioedema. Additionally, we undertake a literature review of HAE.

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Section: Discussionmentioning

confidence: 99%

“…Tranexamic acid, however, was used with success in many studies 5 14 21 33 37–39. The efficacy of injected C1-INH and progesterone contraceptives has not been proven and should be avoided 32…”

Section: Discussionmentioning

confidence: 99%