Rarest of the Rare Metastatic Tubulocystic Carcinoma of Kidney

Abstract

Tubulocystic carcinoma of the kidney is a rare neoplasm with <100 case reports. Patients are usually asymptomatic and have a relatively indolent disease course occurring predominantly in males. These tumors rarely metastasize. It was previously considered to have some similarities to various other renal cancers, although this tumor has distinct macroscopic, microscopic, and immunohistochemical features. It is now a well-established entity in renal neoplastic pathology. Herein we present a case of metastatic tubulocystic carcinoma presenting with bony metastasis.

The Utility of Immunohistochemistry in Diagnosing Tubulocystic Renal Cell Carcinoma with Papillary Morphology

“…Although majority of TC-RCCs behave indolently, there still exist reports of tumor recurrence and distant metastasis. [8][9][10] Given the evolving body of knowledge on TC-RCC, an integrative approach to management becomes imperative to providing optimal care.…”