Rare Tumors

Appendiceal carcinoid tumor with lymph node metastasis in a child: case report and review of the literature

“…The situation changes, however, when one focuses on the published data regarding the age group up to 18 years. Regarding the prognosis of classic solitary childhood AC, there is consensus that no recurrences or tumor-related deaths were observed [10,11]. Besides our patient, we found few other cases of pediatric AC with LNM (Table 1), and up to date, there are no reports of fatalities, recurrences, or disease extension beyond mesenteric LNM in children, regardless of the surgical procedure.…”

“…Currently, the proposed modifications for the German guidelines suggest RHC for PT greater than 1.5 cm [10]. Most other guidelines, such as those cited by Roggo et al [7], Moertel et al [8], and Heij [11], however, suggest performing RHC only when PT is greater than 2 cm, and no recurrences were reported under these conditions in pediatric patients. For AC arising from the base of the appendix, the treatment is controversial (Fig.…”

“…2. There is general consensus that appendectomy alone is considered sufficient for localized disease in the appendix [3,4,7,8,10,11]. The guidelines for children in Germany according to Bucksky et al [4] suggest appendectomy for PT less than 1 cm but require a radical standard RHC resection in cases with PT greater than 1 cm, infiltration of the base or mesentery, as well as lymphatic spread.…”

Intracranial, extradural, hemangiopericytoma in a neonate

“…HPC, a sarcomatous soft-tissue tumor of vascular origin, constitutes only 1% of all vascular tumors. [ 3 ] HPC is commonly seen in the fifth to sixth decades of life; of the 5%–10% cases occurring in childhood, 40% occur in the 1 st year of life. Two distinct clinical entities exist in pediatric HPC.…”