Raghib Syndrome. Surgical Treatment

Pérez-Caballero, Ramón; Izquierdo, Beatriz Plata; Gil-Jaurena, Juan-Miguel

doi:10.1016/j.rec.2015.04.002

Cited by 4 publications

(8 citation statements)

References 0 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…In particular, the studies designed by Caballero 1 and Ueno 3 are similar to our case with detailed explanation of the extracardiac directing of persistent left superior vena cava to the right atrium. In these studies, the authors noted that the extracardiac anastomosis is more effective than intracardiac repair in the presence of complete unroofed coronary sinus.…”

Section: Discussionsupporting

confidence: 79%

See 1 more Smart Citation

Persistent left superior vena cava draining into the unroofed coronary sinus in a patient with tetralogy of Fallot and coronary sinus orifice atresia

Selçuk

Korun²,

Şaşmazel³

2022

Cardiol Young

View full text Add to dashboard Cite

Introduction: In this study, we present a case of directing persistent left superior vena cava drainage into the unroofed coronary sinus to the right atrium in a patient with tetralogy of Fallot and coronary sinus orifice atresia without innominate vein. Case report: A 16-month-old boy diagnosed with tetralogy of Fallot was admitted. Following intracardiac repair, the left superior vena cava was divided from the left atrial junction, passed through under the ascending aorta and anastomosed to the right superior vena cava. Conclusion: To our knowledge, this is the first patient reported with persistent left superior vena cava, unroofed coronary sinus, coronary sinus orifice atresia, and tetralogy of Fallot. The extracardiac direct anastomosis technique was used successfully to direct persistent left superior vena cava to the right atrium without any post-procedure complications

show abstract

Section: Discussionsupporting

confidence: 79%

“…The coexistence of unroofed coronary sinus and persistent left superior vena cava is a rare cardiac anomaly that is known as Raghib syndrome in recognition of the person who first described it. 1 Early diagnosis of this anomaly is important for avoiding brain abscess or brain oedema that can be caused by right-to-left shunt.…”

mentioning

confidence: 99%

Persistent left superior vena cava draining into the unroofed coronary sinus in a patient with tetralogy of Fallot and coronary sinus orifice atresia

Selçuk

Korun²,

Şaşmazel³

2022

Cardiol Young

View full text Add to dashboard Cite

show abstract

“…The use of intracardiac and extracardiac repairs is well documented. 2 , 3 , 4 Concerns of the intracardiac repairs include pulmonary or mitral inflow obstruction and the risk of arrythmias. 3 , 4 Of the extracardiac repair methods, direct anastomosis is preferred because it maintains growth potential and has lower thrombotic complications than synthetic grafts; however, the LSVC has to be long enough to avoid any tension on the anastomosis.…”

Section: Discussionmentioning

confidence: 99%

“… 2 , 3 , 4 Concerns of the intracardiac repairs include pulmonary or mitral inflow obstruction and the risk of arrythmias. 3 , 4 Of the extracardiac repair methods, direct anastomosis is preferred because it maintains growth potential and has lower thrombotic complications than synthetic grafts; however, the LSVC has to be long enough to avoid any tension on the anastomosis. 2 Techniques include anastomosing to the RAA, tunneling through the transverse sinus to the RSVC, and creating a bidirectional left superior cavopulmonary anastomosis with the pulmonary artery.…”

Section: Discussionmentioning

confidence: 99%

Use of 3-dimensionally printed heart models in the planning and simulation of surgery in patients with Raghib syndrome (coronary sinus defect with left superior vena cava)

et al. 2020

View full text Add to dashboard Cite

Raghib syndrome, also known as coronary sinus defect with persistent left superior vena cava (LSVC), consists of complete unroofing of the partial wall between the coronary sinus and the left atrium in the presence of persistent LSVC. 1 It is characterized hemodynamically by drainage of the LSVC to the left atrium and a large interatrial shunt through the ostium of the unroofed coronary sinus. This article describes the use of 3-dimensional (3D) models in the presurgical planning and simulation of 2 patients with Raghib syndrome. PATIENTS AND METHODS Patient ProfilesTwo patients (5 years, 17.6 kg; and 6 years, 16.2 kg) were referred for elective repair of Raghib syndrome. Cross-sectional imaging was performed to depict the patients' anatomy accurately. From these data, 3D-printed models were produced to assist with anatomy interpretation and simulate the technical approaches before the operation (Figure 1). Our Research Ethics Board does not require the patient's consent because there is no identifiable personal health information.

show abstract

“…(1) Alternative surgical strategies could include either: redirecting the PLSVC to the left pulmonary artery as a bidirectional superior cavopulmonary shunt and patching the CS-ASD, or alternatively, as has been more recently described, anastamosing the PLSVC to the right atrial appendage with patch closure of the CS-ASD. (11)…”

Section: Image In Cardiologymentioning

confidence: 99%

An unusual cause for a dilated right heart 33-years post-surgical repair of aortic coarctation

Kyriakakis

Rensburg

Ntusi³

et al. 2018

SAHJ

View full text Add to dashboard Cite

Raghib Syndrome. Surgical Treatment

Cited by 4 publications

References 0 publications

Persistent left superior vena cava draining into the unroofed coronary sinus in a patient with tetralogy of Fallot and coronary sinus orifice atresia

Persistent left superior vena cava draining into the unroofed coronary sinus in a patient with tetralogy of Fallot and coronary sinus orifice atresia

Use of 3-dimensionally printed heart models in the planning and simulation of surgery in patients with Raghib syndrome (coronary sinus defect with left superior vena cava)

An unusual cause for a dilated right heart 33-years post-surgical repair of aortic coarctation

Contact Info

Product

Resources

About