Quadricuspid aortic valve with ruptured sinus of Valsalva

Khan, Shamruz Khan Akerem; Tamin, Syahidah Syed; Burkhart, Harold M.; Araoz, Philip A.; Young, Phillip M.

doi:10.1017/s104795111200042x

Cited by 4 publications

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References 4 publications

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“…1,17 The association of quadricuspid aortic valve with patent ductus arteriosus was first reported in 1923 by Simonds as a postmortem finding. 18 Other associated anomalies are rare and includes coronary artery anomalies, 9 non-obstructive cardiomyopathy, fibromuscular sub-aortic stenosis, 7 rupture sinus of Valsalva, [19][20][21] atrial septal defect, 11,22 partial anomalous pulmonary venous connection, 23 ventricular septal defect, 24 transposition of great arteries, 25 tetralogy of Fallot, 26,27 pulmonary valve stenosis, and congenital complete heart block. Infective endocarditis is also a potential complication 7,11,28 with reported incidence of 1.4%.…”

Section: Discussionmentioning

confidence: 99%

Quadricuspid aortic valve and a large patent ductus arteriosus treated with device closure

2021

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Quadricuspid aortic valve is a remarkably rare congenital cardiac anomaly that predominantly becomes regurgitant with the passage of time. Aortic valve stenosis and aortic root dilatation are less common in quadricuspid aortic valve as compared to bicuspid aortic valve. The clinical presentation depends upon the functional status of the aortic valve, left ventricular function, and associated cardiac or coronary anomalies. The quadricuspid aortic valve is easily visualised during transthoracic echocardiogram with a characteristic X pattern of aortic valve in diastole. The association of quadricuspid aortic valve with patent ductus arteriosus is exceedingly rare. We are reporting a case of young girl with mildly regurgitant quadricuspid aortic valve, large patent ductus arteriosus, and volume-loaded left heart who underwent a successful device closure of her patent ductus arteriosus. To the best of our knowledge, such a case is being reported from Pakistan for the first time.

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