Pulmonary pseudo-tumour, aortitis and IgG4 disease

Abstract

A definitive diagnosis of IgG4-related disease is difficult in patients with intrathoracic or aortic lesions alone. Correlation with specific histopathological findings is essential, regardless of the serum IgG4 concentration, and the number of IgG4-positive plasma cells or the IgG4/IgG ratio in tissue.