Pseudoxanthoma elasticum-like papillary dermal elastolysis. A new case

Vargas-Díez, E

doi:10.1016/0926-9959(95)96200-r

Cited by 10 publications

(11 citation statements)

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“…2,3 Affected sites in PXE-PDE include chiefly flexural areas: the neck; supraclavicular region; scalp; axillae; lower aspect of abdomen/inguinal region; and antecubital fossa. 1,2,[4][5][6][7][8] Mild pruritus can occur in the involved region. The subtle and often asymptomatic clinical presentation may result for patients not seeking medical attention for several years, if at all.…”

Section: Discussionmentioning

confidence: 99%

Fibroelastolytic papulosis

Jagdeo¹,

Ng²,

Ronchetti³

et al. 2004

Journal of the American Academy of Dermatology

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Section: Discussionmentioning

confidence: 99%

Fibroelastolytic papulosis

Jagdeo¹,

Ng²,

Ronchetti³

et al. 2004

Journal of the American Academy of Dermatology

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“…This disease affects more often elderly women and is characterized by asymptomatic and symmetrical yellowish papules localized predominantly on the neck, supraclavicular regions, and flexural areas [2–4]. …”

Section: Discussionmentioning

confidence: 99%

“…The etiopathogenic factors are still unknown but some authors think it can be related with intrinsic skin aging and ultraviolet radiation [2, 5–8]. There is one familial case documented in the literature, suggesting an influence of genetic or inheritable factor [9].…”

Section: Discussionmentioning

confidence: 99%

Pseudoxanthoma Elasticum Papillary Dermal Elastolysis: A Case Report

Alves

Ferreira²,

Vale³

et al. 2010

Dermatology Research and Practice

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PXE-PDE is a rare clinicopathological entity with few cases reported. It affects more often elderly women and is characterized by asymptomatic bilateral and symmetrical yellowish papules localized predominantly on the neck and supraclavicular regions. It is clinically similar to Pseudoxanthoma Elasticum. The authors report a case of a 64-year-old woman presenting asymptomatic, yellowish, non-follicular papules, affecting the occipital and the posterior region of the neck for 1 year. The patient denied pruritic or inflammatory changes, marked solar exposition or trauma on the affected areas. Routine laboratory studies: thoracic x-ray and ophthalmologic examination were normal. The histopathologic examination of a biopsy of one of the cutaneous lesions showed an absence of elastic fibers in the papillary dermis.The diagnosis of Pseudoxanthoma Elasticum—like Papillary Dermal Elastolysis (PXE-PDE) was made. Of great importance is the differential diagnosis with Pseudoxanthoma elasticum (PXE), but we have also to consider other elastolytic disorders: mid-dermal elastolysis (MDE), linear focal elastosis (LFE) and white fibrous papulosis of the neck (WFPN). Until know, there is no effective treatment for this pathology.

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“…Histopathologic examination reveals an atrophic epidermis and bandlike loss of elastic tissue in the papillary dermis (Fig 5, C). 100 Clumping and fragmentation of elastic fibers may also be seen. 98 The reticular dermis is largely unaffected but may show a mild reduction in elastic tissue.…”

Section: Pseudoxanthoma Elasticumÿlike Papillary Dermal Elastolysismentioning

confidence: 96%