Idiopathic intracranial hypertension (IIH) is a condition of elevated intracranial pressure (ICP) of unknown cause. In adults, this is associated with female gender and obesity. Symptoms may include headaches, diplopia, pulsatile tinnitus, and vision loss due to papilledema. Children may develop IIH, although the demographics of prepubescent children with IIH appear to be distinct from older children, being independent of gender and obesity. Recent diagnostic criteria have been established specifically for children with IIH, including a different normal range of ICP in children. Treatments may include weight loss, carbonic anhydrase inhibitors, or surgical procedures. The visual prognosis of children treated appropriately is generally good.