Pseudomyxoma peritonei as an intractable disease and its preoperative assessment to help improve prognosis after surgery: A review of the literature

Zhong, Yi; Deng, Meihai; Xu, Rui‐hua; Kokudo, Norihiro; Tang, Wei

doi:10.5582/irdr.2012.v1.3.115

Cited by 9 publications

(14 citation statements)

References 51 publications

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“…The correct staging of PMP is of great importance if an aggressive surgical approach is to be taken (1,9) . Surgical reduction (debulking) of the tumor and surgery combined with hyperthermic intraperitoneal chemotherapy, with or without chemotherapy in the immediate postoperative period, is recommended at the majority of centers specializing in the management of PMP (1,(10)(11)(12) .…”

Section: Introductionmentioning

confidence: 99%

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The many faces of pseudomyxoma peritonei: a radiological review based on 30 cases

Fonseca¹,

Carvalho²,

Cunha³

et al. 2019

Radiol Bras

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Objective: To determine the most common imaging features of pseudomyxoma peritonei (PMP), as well as the histologic subtypes of the primary tumors. Materials and Methods: We reviewed 30 cases of women with pathologically confirmed PMP. Only computed tomography scans were available. All cases were retrospectively studied by four radiologists, working independently. We identified the most common imaging findings, the predominant primary site of the disease, and the growth pattern. The most common sites of recurrence were also analyzed. Results: The most common computed tomography finding was peritoneal/omental nodules (including “omental caking”), followed by visceral scalloping and non-mucinous ascites. The most common site of the primary tumor was the appendix (in 63.3%), followed by the ovaries (in 16.6%), and 16.6% of the tumors were of undetermined origin. There was one case of synchronous appendiceal and ovarian tumors. Low-grade mucinous neoplasm was the most common histologic subtype, accounting for 84.2% of the appendiceal tumors and 40% of the ovarian tumors. Conclusion: Although PMP is a relatively rare entity, radiologists must be aware of its possible imaging findings, common locations, and possible patterns of recurrence. The origin of the primary tumor should also be investigated. Future studies are needed in order to determine which preoperative imaging findings predict surgical outcomes and to characterize the main findings of radiological recurrence.

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Section: Introductionmentioning

confidence: 99%

“…Imaging is frequently the first step in the diagnosis and management of PMP, with a significant impact on the prognosis (12,13) . Therefore, radiologists should be familiar with the imaging features of the disease.…”

Section: Introductionmentioning

confidence: 99%

The many faces of pseudomyxoma peritonei: a radiological review based on 30 cases

Fonseca¹,

Carvalho²,

Cunha³

et al. 2019

Radiol Bras

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“…According to national data based on population, the annual incidence of PMP is 1,500 cases in the United States of America (USA) and approximately 27 cases or 1.7 to 2 per million per year in the Netherlands. The incidence in Asia is about one per million per year and is presumed to be about a quarter of that in USA [ 1 ]. The occurrence of PMP is slightly higher in women than in men [ 2 – 4 ].…”

Section: Introductionmentioning

confidence: 99%

The RENAPE observational registry: rationale and framework of the rare peritoneal tumors French patient registry

Villeneuve¹,

Passot²,

Gléhen³

et al. 2017

Orphanet J Rare Dis

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BackgroundRare peritoneal cancers represent complex clinical situations requiring a specific and multidisciplinary management. Because of their rarity, lack of awareness and knowledge often leads to diagnostic delays and misdiagnosis. And patients are not systematically referred to expert centers as they should be. Clinicians and researchers also face unique challenges with these rare cancers, because it is hard to conduct adequately powered, controlled trials in such small patient population. This is how an observational patient registry constitutes a key instrument for the development of epidemiological and clinical research in the field of these rare cancers. It is the appropriate tool to pool scarce data for epidemiological research and to assess the impact of diagnostic and therapeutic strategies. We aimed to provide the outlines and the framework of the RENAPE observational registry and share our experience in the establishment of a national patient registry.ResultsThe RENAPE observational registry has been launched in 2010 thanks to institutional supports. It concerns only patients with a histological diagnosis confirming a peritoneal surface malignancy. A web secured clinical database has been implemented based on data management procedures according to the principles of international recommendations and regulatory statements. A virtual tumor bank is linked in order to the conduct translational studies. Specialized working groups have been established to continuously upgrade and evolve the common clinical and histological data elements following the last classifications and clinical practices. They contribute also to standardize clinical assessment and homogenize practices.ConclusionsThe RENAPE Registry may improve awareness and understanding of the rare peritoneal tumors into the incidence, prevalence, recurrence, survival and mortality rates, as well as treatment practices thereby enabling therapeutic intervention to be evaluated and ultimately optimized.Trial registrationClinicalTrials.gov Identifier: NCT02834169

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“…PMP is characterized by diffusely spread collection of gelatinous material into the intra-abdominal cavity along with scattered mucinous implants over peritoneal surfaces and omentum with variable cellularity [ 3 ]. Ronnett et al .…”

Section: Introductionmentioning

confidence: 99%

Pseudomyxoma peritonei with endometrial mucinous carcinoma and appendicular mucinous tumor: An unusual association

Emam

Ghanim

2016

J Microsc Ultrastruct

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The association between pseudomyxoma peritonei and appendicular or ovarian mucinous tumors is usually reported in the literature, while the association with endometrial carcinoma is exceptional. Although there has been always a continuous debate regarding its primary origin, tumors of the appendix and ovary remain the most common primary sites for this disease. The association of pseudomyxoma peritonei with two primaries from endometrial mucinous adenocarcinoma and appendicular mucinous tumor is very rare. So, we report this case to raise awareness among clinicians about this rare tumor association.

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Pseudomyxoma peritonei as an intractable disease and its preoperative assessment to help improve prognosis after surgery: A review of the literature

Cited by 9 publications

References 51 publications

The many faces of pseudomyxoma peritonei: a radiological review based on 30 cases

The many faces of pseudomyxoma peritonei: a radiological review based on 30 cases

The RENAPE observational registry: rationale and framework of the rare peritoneal tumors French patient registry

Pseudomyxoma peritonei with endometrial mucinous carcinoma and appendicular mucinous tumor: An unusual association

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