Pseudocoarctation of the Aorta Associated With Congenital Heart Disease: Report of Ten Cases

Steinberg, Israel; Engle, Mary Allen; Holswade, George R.; Hagstrom, Jack W. C.

doi:10.2214/ajr.106.1.1

Cited by 39 publications

(18 citation statements)

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“…PCoA used to be considered a benign lesion requiring no treatment. Steınberg et al reported that congenital aortic stenosis and pseudocoarctation with four cases in autopsy series [5]. In our patient hemodynamic data and angiography along with physical examination correlated well with these rules.…”

Section: Discussionsupporting

confidence: 85%

Challenging Combination; Pseudocoarctation with Subaortic and Subpulmonic Stenosis

Kırbaş¹

2015

Ann Clin Anal Med

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Anahtar KelimelerPsödokoarktasyon; Aort Stenozu; Kritik Pulmoner Stenoz Abstract Combined left and right ventricular outflow tract obstruction is an extremely rare congenital anomaly. Pseudocoarctation (PcoA), also known as kinking or buckling of the aorta, is an uncommon anomaly of the aorta. A 4-year-old girl presented to our hospital with progressive complaints of exertional dyspnea and intermittent dizziness for about one year. She was diagnosed with severe combined left and right ventricular outflow tract obstructions associated with pseudocoarctation of the aorta. Echocardiographic estimated peek pressure gradients across the right and left ventricular outflow tracts were 151 mmHg and 109 mmHg respectively. There was no significant pressure gradient across the pseudocoarctaion. Aggressive surgical myomectomy for both outflow tracts, combined with reconstruction of right ventricular outflow tract using pericardial patch and iatrogenic ventricular septal defect (VSD) closure using PTFE patch was performed. No intervention was done for pseudocoarctation of the aorta (PcoA). Association of PCoA with different types of cardiac anomalies has been reported. However to our knowledge, combined left and right ventricular outflow obstruction associated with PCoA has not been described before.

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Section: Discussionsupporting

confidence: 85%

Challenging Combination; Pseudocoarctation with Subaortic and Subpulmonic Stenosis

Kırbaş¹

2015

Ann Clin Anal Med

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“…3 Although pseudocoarctation is an isolated anomaly in most cases, and regarded as a benign entity, a variety of abnormalities associated with it have been reported, including bicuspid aortic valve, aortic stenosis, ventricular septal defect, atrial septal defect, patent ductus arteriosus, and sinus of Valsalva aneurysm. 6 In addition, pseudocoarctation has been associated with aneurysm formation of the thoracic aorta, which causes sudden rupture or dissection. 7 In our patient, the aneurysm was found as a saccular formation, and the aneurysmal wall was partially thinned.…”

Section: Discussionmentioning

confidence: 99%

Pseudocoarctation of the aorta complicated by thoracic aortic aneurysm

Kimura

Ohtake

Kato

et al. 2011

Asian Cardiovasc Thorac Ann

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Pseudocoarctation is a rare anomaly involving kinking or buckling of the aorta without a pressure gradient across the lesion, considered to be a benign entity warranting no specific intervention. An uncommon case of pseudocoarctation associated with aortic aneurysm formation in 21-year-old woman is described. Pathological findings suggested that the etiology was anomalous development of the aorta in association with pseudocoarctation; therefore, careful follow-up of patients affected by pseudocoarctation is mandatory.

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“…As a result, the aortic arch is longer than normal, and eventually twists or kinks at the point of insertion of the ligamentum arteriosum. Pseudocoarctation may also result from a short, taut ligamentum arteriosum or PDA (77).…”

Section: Pseudocoarctationmentioning

confidence: 99%

Congenital Variants and Anomalies of the Aortic Arch

Hanneman¹,

Newman²,

Chan³

2017

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307

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Congenital variants and anomalies of the aortic arch are important to recognize as they may be associated with vascular rings, congenital heart disease, and chromosomal abnormalities, and can have important implications for prognosis and management. The purpose of this article is to review cross-sectional imaging techniques used in the evaluation of the aortic arch, describe the embryology and anatomy of the aortic arch system, discuss aortic arch variants and anomalies, and review other malformations of the aortic arch, including interrupted aortic arch, hypoplastic aortic arch, and aortic coarctation. Aortic arch variants and anomalies will be reviewed in the context of a theoretical double aortic arch system. Arch anomalies can be associated with symptoms, such as dysphagia lusoria in the setting of left aortic arch with aberrant right subclavian artery. Arch variants that form a vascular ring, such as double aortic arch, can result in respiratory distress due to tracheal compression. Certain arch anomalies are strongly associated with congenital heart disease, including right aortic arch with mirror image branching. Other malformations of the aortic arch have important associations, such as type B interrupted aortic arch, which is associated with a locus 22q11.2 microdeletion. Noninvasive imaging at CT angiography and MR angiography allows for comprehensive evaluation of the aortic arch and branch vessels in relation to surrounding structures. Familiarity with the spectrum and imaging appearances of aortic arch variants, anomalies, and malformations is essential for accurate diagnosis and classification and to guide management. Online supplemental material is available for this article. RSNA, 2016.

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Pseudocoarctation of the Aorta Associated With Congenital Heart Disease: Report of Ten Cases

Cited by 39 publications

References 0 publications

Challenging Combination; Pseudocoarctation with Subaortic and Subpulmonic Stenosis

Challenging Combination; Pseudocoarctation with Subaortic and Subpulmonic Stenosis

Pseudocoarctation of the aorta complicated by thoracic aortic aneurysm

Congenital Variants and Anomalies of the Aortic Arch

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