Prune belly syndrome, a rare case presentation in neonatology: about one case in Yaounde, Cameroon

Abstract

The Prune-Belly syndrome (PBS) is a rare pathology predominating in male infants, classically manifesting with the triad including aplasia of the abdominal wall muscles, dilatation of the urinary tract, and testicular abnormalities. We report and discuss the case of a full-term male newborn, in whom clinical examination at birth revealed abdominal wall muscle hypoplasia, cryptorchidism, urinary tract dilatation and renal failure. The diagnosis was made based on physical assessment, abdominal ultra-sonographic imaging, and blood sampling of urea and creatinine. For such cases, the recommended surgical management usually consists in a sequential surgical intervention including urinary tract reconstruction, abdominoplasty, and orchidopexy. However, these could not be practiced in due time in our patient, who died on the seventh day of life because of kidney failure. The prognosis of infants with Prune-Belly syndrome may be improved by quality antenatal follow-up, to enable the early diagnosis and preparation for prompt surgical intervention.

Macrosomia: A Risk Factor of Childhood Obesity: A Case Report with Literature Review

“…This is a condition which requires effective perinatal and deep neonatal assessments, given potential complications. More so, there was maternal obstetrical history of big babies, which was predisposing to macrosomia as well, and a contributing finding [6][7][8][9][10][11][12][13][14][15][16][17][18][19].…”

The Baby Blues and Perinatal Psychic Disorders: About Prevention and Management

“…This contributes to reassuring the mother and her partner, preventing worries and anxiety. It also helps to anticipate problems and challenges, so as to better manage them and avoid last-minute surprises [22][23][24][25][26][27][28][29][30]. In effect, in case a congenital birth defect or malformation is early diagnosed, parents' assistance with a psychologist is indispensable and should absolutely be recommended by the physician.…”

“…In effect, in case a congenital birth defect or malformation is early diagnosed, parents' assistance with a psychologist is indispensable and should absolutely be recommended by the physician. This will facilitate gradual acceptance of the diagnosis, with the understanding of embryo-fetopathy, conditioning and coping, motivation to continue visits, and treatment observance [15][16][17][18][19][20][21][22][23][24][25][26][27][28][29][30][31][32][33].…”

Investigating the Psychosocial Dimension of Perinatality in Cameroon

“…In effect, the changes of the woman's body image require time for the structuration and modulation of maternal representations of new appearances, feelings and emotions [1][2][3][4][5][6]. Moreover, the conscious acquaintance with protecting a fragile being developing from within oneself is paramount as well [15][16][17][18][19][20][21][22][23][24][25][26]. A mental representation could be considered as a thoughtful selfpresentation and interpretation of a particular situation or event, constituting the content of the thought.…”

“…Besides psychosomatic issues of perinatality, there are preoccupations with social impressions, apprehensions, judgment and weight of parental responsibility. It is well known that pregnant women experience recurrent phantasmagoric thoughts over the baby physical appearance [15][16][17][18][19][20][21][22][23][24][25][26]. Furthermore, mothers' minds question paternal adoption capacity, acceptation and responsibility, as well as the reliability of relatives, entourage, and worries with the future social insertion of the growing infant [27][28][29][30][31].…”