Background:Malignant proliferating trichilemmal tumor is a rare skin tumor that affects mainly older women. It similar to differential squamous cell carcinoma. Methods: A search strategy was designed and run in Medline and google scholar. Also, searching grey literature, checking references, tracking citations, hand-searching of focused journals, and websites were utilized for retrieval of related studies. All of articles which studied epidemiology of mortality or injuries of the war were included. Conclusion:Malignant proliferating trichilemmal tumours are rare and cause struggling in diagnosis for the surgeon as there is a high risk of recurrence and metastasis