Progressive Scoliosis in a Child with Cystic Fibrosis

Castner, Lauren M; Nasr, Samya Z.; Arteta, Manuel

doi:10.1155/2019/1471879

Cited by 1 publication

(1 citation statement)

References 10 publications

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“…The chronological classification is important in quantifying the risk of developing a more severe and complicated deformity, while the angular classification is crucial in the management of IS since it is directly correlated with treatment decisions [ 16 , 17 , 18 ]. Scoliosis in CF has been previously investigated [ 11 , 14 , 19 , 20 , 21 , 22 ], and most authors have found that in these patients its prevalence is higher compared to the healthy population, where the prevalence ranges from 0.2 to 2.2% with a preference for girls, especially in older age and when the curve is higher [ 23 , 24 ]. On the other hand, kyphosis is an excessive curvature of the thoracic spine in the standing position.…”

Section: Introductionmentioning

confidence: 99%

Prevalence of Scoliosis in Children and Adolescents with Cystic Fibrosis

Fainardi,

Nora,

Salghetti

et al. 2024

Children

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The prevalence of scoliosis in people with cystic fibrosis (CF) seems to be greater than in the normal population. Over the last two years, a screening for spinal deformities was carried out in patients with CF aged 5 to 18 years, followed up at the CF regional Centre in Parma (Italy). Forty-three patients (twenty-seven males, mean age: 11.8 ± 4.5 years) were enrolled in the study. Nine patients (20.9%) were diagnosed with scoliosis, with a mean Cobb angle of 20.8 ± 9.4 (12–38°). Five patients (11.6%) were diagnosed with a postural kyphosis attitude and one with pathological fixed kyphosis. All patients with scoliosis and postural kyphosis started daily physiotherapeutic scoliosis-specific exercises (PSSE). Compared to people without CF, the prevalence of scoliosis in our paediatric CF population seems to be higher and more present in males; the curves were thoracic and mostly right-sided. CF disease, hyposthenic postural attitude and sedentary lifestyle can contribute to the pathogenesis of this musculoskeletal alteration. Spinal deformities may negatively affect pulmonary function, resulting in disability, pain and a decreased quality of life. Since the prevention of musculoskeletal deformities is easier than restoration, in CF population targeted screening during growth and interventions, including regular physical exercise, are mandatory.

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