Primitive Neuroectodermal Tumor of Maxilla: A Rare Case

Kadagad, Poornima; Umarani, M.; Pinto, Pascal X.

doi:10.5005/jp-journals-10015-1098

Cited by 3 publications

(2 citation statements)

References 12 publications

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“…Distant metastases are determined in 20 to 25% of newly diagnosed patients, especially bone and bone marrow metastases The most common sites of metastasis include the lung, bone, and bone marrow. 24 Because of high metastases rate, a detailed clinical and radiological evaluation is necessary of PNET. Chest radiograph, bone scintigraphy can be used to determine the metastasis.…”

Section: Discussionmentioning

confidence: 99%

Imaging Features of Primitive Neuroectodermal Tumor in the Maxilla: A Case Report and Literature Review

Bozdemir¹,

Fındık²,

Bilgir³

et al. 2016

Turkiye Klinikleri J Dental Sci Cases

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106rimitive neuroectodermal tumor (PNET) is a term used to describe a group of highly rare and malignant neoplasms composed of undifferentiated round cell tumors of neuroectodermal origin with variable cell differentiation. PNET generally occurs in the central nervous system (CNS); peripheral PNET occurring outside the CNS has also been reported. Peripheral PNET is commonly related to Ewing's sarcoma (ES). However, it exhibits a more aggressive clinical behavior than ES, with extremely rapid metastasis. PNET has a poor prognosis and is commonly seen in children and young adults.1 Because this tumor presents aggressive biological behavior and tends toward loco-regional and systemic metastases, it is a tumor with an extremely poor survival rate.2 The incidence of head and neck PNET Imaging Features of Primitive Neuroectodermal Tumor in the Maxilla: A Case Report and Literature Review A AB BS S T TR RA AC CT T Primitive neuroectodermal tumor (PNET) is a term used to describe a group of highly malignant neoplasms composed of undifferentiated round cell tumors of neuroectodermal origin with variable cell differentiation. PNET generally occurs in the central nervous system (CNS), but peripheral PNET occurring outside the CNS has also been reported. The most common location of PNET in head and neck region is the orbit, followed by the neck and the parotid gland. PNET of the maxilla is rare. The aims of this report are to present the case of a 41-year-old female diagnosed with PNET tumor of the maxilla after detailed clinical, radiological, and histopathological examinations and to review the previously reported cases of PNET of the maxilla in the literature.K Ke ey y W Wo or rd ds s: : Neuroectodermal tumors, primitive, peripheral; maxilla; diagnosis; cone-beam computed tomography Ö ÖZ ZE ET T Primitif nöroektodermal tümör (PNET), nöroektodermal kökenli farklılaşmamış yuvarlak hücreli tümörlerden oluşan son derece malign tümörlerin bir grubunu tanımlamak için kullanılan bir terimdir. PNET genellikle santral sinir sisteminde meydana gelir fakat santral sinir sistemi dışında ortaya çıkan periferal PNET olguları da rapor edilmiştir. Baş-boyun bölgesinde en fazla gözde görülür. Gözden sonra en sık boyun ve parotis bezinde görülür. Maksilladaki PNET nadirdir. Bu raporun amacı detaylı klinik, radyolojik ve histopatolojik incelemeden sonra maksillada PNET tanısı koyulan 41 yaşında kadın hastayı sunmak ve literatürde daha önce rapor edilen maksilladaki PNET vakalarını incelemektir.A An na ah h t ta ar r K Ke e l li i m me e l le er r: : Nöroektodermal tümörler, primitif, periferik; maksilla; tanı; konik ışınlı bilgisayarlı tomografi T Tu ur rk ki iy ye e K Kl li in ni ik kl le er ri i J J D De en nt ta al l S Sc ci i C Ca as se es s 2 20 01 16 6; ;2 2( (3 3) ): :1 10 06 6--1 12 2

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Section: Discussionmentioning

confidence: 99%

Imaging Features of Primitive Neuroectodermal Tumor in the Maxilla: A Case Report and Literature Review

Bozdemir¹,

Fındık²,

Bilgir³

et al. 2016

Turkiye Klinikleri J Dental Sci Cases

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“…Primitive neuroectodermal tumor (PNET) was first described by Hart and Earle in 1973 [2]. It is a small round cell tumor of presumed neural crest origin arising outside the central and sympathetic nervous system with variable differentiation [3]. Though primitive neuroectodermal tumors occur predominantly in central nervous system, peripheral PNETs have also been reported [4].…”

Section: Introductionmentioning

confidence: 99%

A rare case of peripheral primitive neuroectodermal tumor in palate

Ranka¹,

Jain²,

Gadbail³

et al. 2019

Surg Rehabil

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Primitive Neuroectodermal Tumor (PNET) is an aggressive round cell malignant tumor which belongs to Ewing's Sarcoma family. Peripheral PNET is rare in head and neck region and even rare in palate with handful of cases reported till date. A case of Peripheral PNET of palate in a 32-year-old female pa tient along with its clinico-pathologic, radiologic and immunohistologic features as well as its management is reported here. We emphasize the need of histopathology and immunohistochemistry (IHC) for early diagnosis of such aggressive tumors to improve the prognosis of patient by providing timely management.

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Case Report: Cytodiagnosis of primitive neuroectodermal tumor (PNET) of sinonasal tract

Khan,

Bhake

2023

F1000Res

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Malignant sinonasal tumors are rarely encountered in the practice of oncology as they constitute only 1% of total body tumors. The occurrence of primitive neuroectodermal tumor (PNET) in the sinonasal tract is even more uncommon. The PNET belongs to Ewing sarcoma family and forms the differential diagnosis of a large group of lesions generally described as malignant round cell tumors. The unique pathogenetic chromosomal alteration in this lesion is the EWS FLI1 fusion gene. This case report describes the unusual occurrence of PNET for its cytomorphological diagnosis along with its clinical features, radioimaging findings and immunohistochemistry. Such case reports are scarce in literature and cytodiagnosis of PNET in sinonasal tracts warrants its sharing with medical fraternity as such diagnoses are stumbled along rarely in clinical practice.

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Primitive Neuroectodermal Tumor of Maxilla: A Rare Case

Cited by 3 publications

References 12 publications

Imaging Features of Primitive Neuroectodermal Tumor in the Maxilla: A Case Report and Literature Review

Imaging Features of Primitive Neuroectodermal Tumor in the Maxilla: A Case Report and Literature Review

A rare case of peripheral primitive neuroectodermal tumor in palate

Case Report: Cytodiagnosis of primitive neuroectodermal tumor (PNET) of sinonasal tract

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