Primary undifferentiated embryonal sarcoma of the liver misdiagnosed as hydatid cyst in a child: case report and review of the literature

Halefoğlu, AM; Öz, Abdullah Bahadır

doi:10.5334/jbr-btr.91

Cited by 3 publications

(4 citation statements)

References 18 publications

Supporting

Mentioning

Contrasting

Unclassified

Order By: Relevance

“…This diagnostic pitfall may cause delayed management. There have been several case reports of UESL being mistaken for hydatid disease [ 18 , 19 ]. Discrepancy of internal architecture on US and CT was considered one of the important characteristics of UESL.…”

Section: Discussionmentioning

confidence: 99%

Pulmonary Metastases from an Undifferentiated Embryonal Sarcoma of the Liver: A Case Report and Review

Shi

Sangster

et al. 2018

Case Reports in Oncological Medicine

View full text Add to dashboard Cite

Undifferentiated embryonal sarcoma of the liver (UESL) is a rare malignant hepatic tumor that occurs primarily in children. Only a limited number of cases have been reported in the literature due to low incidence of one per million, and reports of metastatic lesion of UESL are even rarer. We hereby describe the case of a 13-year-old male who presented with a palpable mass with imaging findings suggestive of a large complex tumor in the right lobe of the liver. He underwent extended right hepatectomy followed by adjuvant chemotherapy. The tumor was confirmed to be UESL by postoperative pathology and immunohistochemical staining analysis. Four years later, surveillance imaging revealed a small lung nodule in the left lower lobe. Complete removal of the lung tumor by wedge resection was performed, and a histological diagnosis of metastatic UESL was made. The patient also received postoperative adjuvant chemotherapy and is currently in a good general condition and tumor-free in the present eight-month period. This case is presented with emphasis on clinicopathological and immunohistochemical findings of the primary UESL and lung metastases with the aim of collecting more data and expanding our understanding of this rare malignancy.

show abstract

Section: Discussionmentioning

confidence: 99%

Pulmonary Metastases from an Undifferentiated Embryonal Sarcoma of the Liver: A Case Report and Review

Shi

Sangster

et al. 2018

Case Reports in Oncological Medicine

View full text Add to dashboard Cite

show abstract

“…Известно об орган-сохраняющей резекции с возможной абляцией остаточной кисты с использованием электрокоагуляции [16]. Также возможно альтернативное оперативное вмешательство в объеме энуклеации кисты при невозможности радикальной резекции или риске развития значительных периоперационных осложнений [17].…”

Section: заболеваемостьunclassified

“…Билиарные ЦАК, в отличие от ЦА, чаще встречаются у пожилых пациентов мужского пола с менее продолжительной клинической картиной. Хотя симптомы билиарной ЦА и ЦАК похожи, значительная разница отмечается с точки зрения возраста, пола, уровня билирубина, АЛТ, размера опухоли и наличия пристеночных узлов [17]. Более высокие уровни ферментов у пациентов с ЦАК наблюдаются из-за инвазии опухоли в соседние желчные протоки, в то время как ЦА является медленно растущим образованием и вызывает позднее сдавление желчевыводящих путей.…”

Section: во фрагменте ткани печени опухолевый узел имеет строение сли...unclassified

Diagnostic and Treatment Errors in Biliary Cystadenomas and Cystadenocarcinomas: Clinical Cases

Ayvazyan¹,

Kuzminikh²,

Shevchenko³

et al. 2022

Kuban. nauсh. med. vestnik

View full text Add to dashboard Cite

Background. Biliary cystadenomas and cystadenocarcinomas are rare cystic tumors of the liver. Complicated differential diagnostics for simple cysts often leads to errors in surveillance of patients with these tumors. Cystadenoma and cystadenocarcinoma should be suspected upon detection of single or multilocular cystic neoplasms of the liver with septa and blood flow loci in the cyst wall, especially in middle-aged women. The localization of the tumor is critical. The most common localization is segment IV of the liver. Urgent intraoperative biopsy is required to determine the extent of surgery.Case description. Clinical observations with analysis of the examination and treatment data of two female patients aged 38 and 56 were presented. Both clinical observations illustrate the underestimation of the preoperative examination data that served as a ground for diagnosis of liver cysts with inadequate extent of surgery. In the first case, the resection was incomplete, and, as such, the biliary cystadenoma recurred in the resection area, the capsule of the neoplasm was ruptured and an encysted fluid collection was formed. In the second case, lack of histological examination of the excised neoplasm, due to confidence in its morphological verification as a cyst, resulted in cystadenoma recurrence in the resection zone with metastasis to the contralateral lobe of the liver.Conclusion. Hepatic cystadenomas and cystadenocarcinomas are often misdiagnosed as simple cysts. These tumors should be suspected in central localization of the tumor in the liver, especially in young women. The clinical and instrumental symptomatology and radiological semiotics of the disease require careful evaluation. The recurrence of a cystic lesion in the resection zone in a patient previously operated for a hepatic cyst serves as an additional signal for detecting biliary cystadenoma. Rational strategy for surgical management of cystic liver lesions should include hepatectomy within healthy tissues (both anatomical and atypical) with mandatory intraoperative ultrasound and urgent histological examinations.

show abstract

“…Bilgisayarlı tomografi, kistin kalsifikasyonu ve enfeksiyonu ile birlikte periton ve akciğer gibi diğer organ kistlerini göstermede daha etkili olmakla birlikte kist içeriğini göster-mede ve tiplendirmede yetersiz kalabilir (Resim 1) [2]. Uyumlu hastalarda manyetik rezonans görüntüleme ile kist içeriği daha iyi gösterilebi-lir ve radyasyon içermemesi sebebiyle özellikle perkütan tedavi sonrası takiplerde daha uygundur.…”

unclassified

Perkütan Karaciger Kist Hidatik Tedavisi

Eren¹,

Kantarcı²

2015

Trd Sem

View full text Add to dashboard Cite

Primary undifferentiated embryonal sarcoma of the liver misdiagnosed as hydatid cyst in a child: case report and review of the literature

Cited by 3 publications

References 18 publications

Pulmonary Metastases from an Undifferentiated Embryonal Sarcoma of the Liver: A Case Report and Review

Pulmonary Metastases from an Undifferentiated Embryonal Sarcoma of the Liver: A Case Report and Review

Diagnostic and Treatment Errors in Biliary Cystadenomas and Cystadenocarcinomas: Clinical Cases

Perkütan Karaciger Kist Hidatik Tedavisi

Contact Info

Product

Resources

About