BackgroundTwin ectopic pregnancy is a rare disease. Herein we report a rare case of spontaneous caesarean scar pregnancy co-existing with tubal pregnancy, and review the relevant literature with respect to treatments.Case presentationA 36-year-old female was admitted to our hospital with complaints of 48 days of menopause and 20 days of vaginal bleeding. Physical examinations and medically assisted examinations suggested the existence of spontaneous caesarean scar pregnancy co-existing with tubal pregnancy. The patient underwent laparoscopic left retrograde salpingectomy and excision of the caesarean scar pregnancy. The patient recovered well during outpatient follow-ups.ConclusionsDue to the rarity and particularity of spontaneous caesarean scar associated with ectopic tubal twin pregnancy, accurate diagnosis preoperatively seems particularly difficult. During this report, the possibility of twin ectopic pregnancy should be borne in mind in order to avoid missed diagnosis when meeting women of gestational age who have menopause.